Progressive leukoencephalopathy as a manifestation of primary angiitis of the central nervous system: case report and review of the literature.
J Neurol
; 271(6): 3648-3652, 2024 Jun.
Article
em En
| MEDLINE
| ID: mdl-38478031
ABSTRACT
BACKGROUND AND OBJECTIVE:
Primary angiitis of the central nervous system (PACNS) is a rare form of vasculitis solely affecting the vessels of the brain, spinal cord, and leptomeninges. A range of magnetic resonance imaging (MRI) features have been associated with PACNS, including cerebral infarction, hemorrhage, and parenchymal or leptomeningeal contrast enhancement. METHODS ANDRESULTS:
We describe a 51-year-old man with a case of PACNS manifesting as akinetic mutism with progressive leukoencephalopathy.DISCUSSION:
Progressive leukoencephalopathy has not been well defined as a manifestation of PACNS. We review a small number of cases with comparable features, providing additional context on this PACNS manifestation with consideration of clinical subtypes.Palavras-chave
Texto completo:
1
Bases de dados:
MEDLINE
Assunto principal:
Vasculite do Sistema Nervoso Central
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Leucoencefalopatias
Limite:
Humans
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Male
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Middle aged
Idioma:
En
Revista:
J Neurol
/
J. neurol
/
Journal of neurology
Ano de publicação:
2024
Tipo de documento:
Article
País de afiliação:
Estados Unidos