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Biliary atresia in a 3-month-old infant (case report).
Paviglianiti, Giuseppe; Avallone, Roberta Cristina; Cariello, Valentina; Vaccaro, Marzia; Di Marco, Floriana; Minelli, Rocco; De Chiara, Francesca Antonia; Esposito, Francesco; Ferrara, Dolores; Rossi, Antonio; Pizzicato, Paolo; Rossi, Eugenio.
Afiliação
  • Paviglianiti G; U.O.C. Pediatric Radiology P.O.G. Di Cristina - ARNAS Civico-Di Cristina-Benfratelli, Palermo, Italy.
  • Avallone RC; Department of Precision Medicine, University of Campania "L. Vanvitelli", Naples, Italy. robertacristina.avallone@gmail.com.
  • Cariello V; Department of Precision Medicine, University of Campania "L. Vanvitelli", Naples, Italy.
  • Vaccaro M; Department of Precision Medicine, University of Palermo "P. Giaccone", Palermo, Italy.
  • Di Marco F; Health District 42 of ASP Palermo, Palermo, Italy.
  • Minelli R; Department of Medicine and Health Sciences "V. Tiberio", University of Molise, Campobasso, Italy.
  • De Chiara FA; Department of Medicine and Health Sciences "V. Tiberio", University of Molise, Campobasso, Italy.
  • Esposito F; U.O.S.D. Diagnostic Imaging P.O. Santobono - AORN Santobono-Pausilipon, Naples, Italy.
  • Ferrara D; U.O.S.D. Diagnostic Imaging P.O. Santobono - AORN Santobono-Pausilipon, Naples, Italy.
  • Rossi A; University "Campus Biomedico", Rome, Italy.
  • Pizzicato P; U.O.S.D. Diagnostic Imaging P.O. Pausilipon - AORN Santobono-Pausilipon, Naples, Italy.
  • Rossi E; U.O.S.D. Diagnostic Imaging P.O. Pausilipon - AORN Santobono-Pausilipon, Naples, Italy.
J Ultrasound ; 27(3): 739-743, 2024 Sep.
Article em En | MEDLINE | ID: mdl-39026132
ABSTRACT
Biliary atresia (BA) is a congenital disease that occurs when extrahepatic bile ducts are either absent or deficient, resulting in liver fibrosis, portal hypertension, and eventually cirrhosis. It is the most common cause of persistent obstructive jaundice in newborns lasting more than two weeks is this condition. Abdominal ultrasound (US) is the primary imaging technique used to diagnose BA, while computed tomography (CT) is reserved for more complex cases. The gold standard for diagnosing BA is still intraoperative cholangiogram with liver biopsy. Treatment for BA usually involves Kasai hepatoportoenterostomy, but some patients still require liver transplantation due to diagnostic delays and advanced disease. In this study, the authors present the case of a 3-month-old infant with biliary atresia and its ultrasound characteristics, who underwent liver transplantation due to advanced disease. The primary objective of imaging is to provide a prompt diagnosis, given the crucial significance of timely surgical intervention.
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Texto completo: 1 Bases de dados: MEDLINE Assunto principal: Atresia Biliar / Ultrassonografia / Transplante de Fígado Limite: Female / Humans / Infant / Male Idioma: En Revista: J Ultrasound Ano de publicação: 2024 Tipo de documento: Article País de afiliação: Itália

Texto completo: 1 Bases de dados: MEDLINE Assunto principal: Atresia Biliar / Ultrassonografia / Transplante de Fígado Limite: Female / Humans / Infant / Male Idioma: En Revista: J Ultrasound Ano de publicação: 2024 Tipo de documento: Article País de afiliação: Itália