[Postoperative fructose infusion in a case of presumed hereditary fructose intolerance (author's transl)]. / Postoperative Fruktoseinfusion bei wahrscheinlich hereditärer Fruktoseintoleranz.
Wien Klin Wochenschr
; 90(7): 237-40, 1978 Mar 31.
Article
em De
| MEDLINE
| ID: mdl-76370
ABSTRACT
Hereditary fructose intolerance (HFI) was diagnosed in a 61 year-old male patient on account of liver dysfunction followed by prolonged shock immediately after the administration of a fructose and lactose infusion postoperatively. The diagnosis of HFI was based on an increased value of fructose, hypoglycaemia, lactic acidosis and diminution of the phosphate level in combination with the typical family history. The patient's children showed a normal reaction to fructose administration. The therapy included glucose, insulin and heparin administration, balance of acidosis and partial exchange of blood, which resulted in improvement in the glucose level, coagulation factors and acidosis, but could not prevent further liver damage and uraemia with a fatal outcome.
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Bases de dados:
MEDLINE
Assunto principal:
Erros Inatos do Metabolismo dos Carboidratos
/
Intolerância à Frutose
/
Encefalopatia Hepática
/
Frutose
Limite:
Humans
/
Male
/
Middle aged
Idioma:
De
Revista:
Wien Klin Wochenschr
Ano de publicação:
1978
Tipo de documento:
Article