Detalhe da pesquisa
1.
CFTR and PC2, partners in the primary cilia in autosomal dominant polycystic kidney disease.
Am J Physiol Cell Physiol
; 325(3): C682-C693, 2023 09 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-37519231
2.
A new role for heat shock factor 27 in the pathophysiology of Clostridium difficile toxin B.
Am J Physiol Gastrointest Liver Physiol
; 318(1): G120-G129, 2020 01 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-31709831
3.
Restoration of F508-del Function by Transcomplementation: The Partners Meet in the Endoplasmic Reticulum.
Cell Physiol Biochem
; 52(6): 1267-1279, 2019.
Artigo
em Inglês
| MEDLINE | ID: mdl-31026390
4.
Histone deacetylase 6 inhibition reduces cysts by decreasing cAMP and Ca2+ in knock-out mouse models of polycystic kidney disease.
J Biol Chem
; 292(43): 17897-17908, 2017 10 27.
Artigo
em Inglês
| MEDLINE | ID: mdl-28887310
5.
Syntaxin 8 and the Endoplasmic Reticulum Processing of ΔF508-CFTR.
Cell Physiol Biochem
; 51(3): 1489-1499, 2018.
Artigo
em Inglês
| MEDLINE | ID: mdl-30485852
6.
Combination of Correctors Rescue ΔF508-CFTR by Reducing Its Association with Hsp40 and Hsp27.
J Biol Chem
; 290(42): 25636-45, 2015 Oct 16.
Artigo
em Inglês
| MEDLINE | ID: mdl-26336106
7.
Rescuing Trafficking Mutants of the ATP-binding Cassette Protein, ABCA4, with Small Molecule Correctors as a Treatment for Stargardt Eye Disease.
J Biol Chem
; 290(32): 19743-55, 2015 Aug 07.
Artigo
em Inglês
| MEDLINE | ID: mdl-26092729
8.
Inhibition of histone deacetylase 6 activity reduces cyst growth in polycystic kidney disease.
Kidney Int
; 90(1): 90-9, 2016 07.
Artigo
em Inglês
| MEDLINE | ID: mdl-27165822
9.
STIM1fl/fl Ksp-Cre Mouse has Impaired Renal Water Balance.
Cell Physiol Biochem
; 39(1): 172-82, 2016.
Artigo
em Inglês
| MEDLINE | ID: mdl-27336410
10.
CFTR Controls the Activity of NF-κB by Enhancing the Degradation of TRADD.
Cell Physiol Biochem
; 40(5): 1063-1078, 2016.
Artigo
em Inglês
| MEDLINE | ID: mdl-27960153
11.
Regulation of CFTR Expression and Arginine Vasopressin Activity Are Dependent on Polycystin-1 in Kidney-Derived Cells.
Cell Physiol Biochem
; 38(1): 28-39, 2016.
Artigo
em Inglês
| MEDLINE | ID: mdl-26741910
12.
Correctors Rescue CFTR Mutations in Nucleotide-Binding Domain 1 (NBD1) by Modulating Proteostasis.
Chembiochem
; 17(6): 493-505, 2016 Mar 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-26864378
13.
Gout-causing Q141K mutation in ABCG2 leads to instability of the nucleotide-binding domain and can be corrected with small molecules.
Proc Natl Acad Sci U S A
; 110(13): 5223-8, 2013 Mar 26.
Artigo
em Inglês
| MEDLINE | ID: mdl-23493553
14.
Mis-regulation of mammalian target of rapamycin (mTOR) complexes induced by albuminuria in proximal tubules.
J Biol Chem
; 289(24): 16790-801, 2014 Jun 13.
Artigo
em Inglês
| MEDLINE | ID: mdl-24790108
15.
Polycystin-1 negatively regulates Polycystin-2 expression via the aggresome/autophagosome pathway.
J Biol Chem
; 289(10): 6404-6414, 2014 Mar 07.
Artigo
em Inglês
| MEDLINE | ID: mdl-24459142
16.
Overcoming the cystic fibrosis sputum barrier to leading adeno-associated virus gene therapy vectors.
Mol Ther
; 22(8): 1484-1493, 2014 Aug.
Artigo
em Inglês
| MEDLINE | ID: mdl-24869933
17.
Transcomplementation by a truncation mutant of cystic fibrosis transmembrane conductance regulator (CFTR) enhances ΔF508 processing through a biomolecular interaction.
J Biol Chem
; 288(15): 10505-12, 2013 Apr 12.
Artigo
em Inglês
| MEDLINE | ID: mdl-23463513
18.
Future directions in early cystic fibrosis lung disease research: an NHLBI workshop report.
Am J Respir Crit Care Med
; 185(8): 887-92, 2012 Apr 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-22312017
19.
Drosophila TRPA1 channel mediates chemical avoidance in gustatory receptor neurons.
Proc Natl Acad Sci U S A
; 107(18): 8440-5, 2010 May 04.
Artigo
em Inglês
| MEDLINE | ID: mdl-20404155
20.
Transduction of Ferret Surface and Basal Cells of Airways, Lung, Liver, and Pancreas via Intratracheal or Intravenous Delivery of Adeno-Associated Virus 1 or 6.
Hum Gene Ther
; 34(21-22): 1135-1144, 2023 Nov.
Artigo
em Inglês
| MEDLINE | ID: mdl-37650819