Detalhe da pesquisa
1.
Survival in primary hemophagocytic lymphohistiocytosis, 2016 to 2021: etoposide is better than its reputation.
Blood
; 143(10): 872-881, 2024 Mar 07.
Artigo
em Inglês
| MEDLINE | ID: mdl-37992218
2.
Genotype, oxidase status, and preceding infection or autoinflammation do not affect allogeneic HCT outcomes for CGD.
Blood
; 142(24): 2105-2118, 2023 12 14.
Artigo
em Inglês
| MEDLINE | ID: mdl-37562003
3.
Posttransplantation late complications increase over time for patients with SCID: A Primary Immune Deficiency Treatment Consortium (PIDTC) landmark study.
J Allergy Clin Immunol
; 153(1): 287-296, 2024 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-37793572
4.
Allogeneic hematopoietic cell transplantation is effective for p47phox chronic granulomatous disease: A Primary Immune Deficiency Treatment Consortium study.
J Allergy Clin Immunol
; 153(5): 1423-1431.e2, 2024 May.
Artigo
em Inglês
| MEDLINE | ID: mdl-38290608
5.
Relevance of lymphocyte proliferation to PHA in severe combined immunodeficiency (SCID) and T cell lymphopenia.
Clin Immunol
; 261: 109942, 2024 04.
Artigo
em Inglês
| MEDLINE | ID: mdl-38367737
6.
Quercetin ameliorates XIAP deficiency-associated hyperinflammation.
Blood
; 140(7): 706-715, 2022 08 18.
Artigo
em Inglês
| MEDLINE | ID: mdl-35687753
7.
T-follicular helper cell expansion and chronic T-cell activation are characteristic immune anomalies in Evans syndrome.
Blood
; 139(3): 369-383, 2022 01 20.
Artigo
em Inglês
| MEDLINE | ID: mdl-34424963
8.
Intestinal microbiome and metabolome signatures in patients with chronic granulomatous disease.
J Allergy Clin Immunol
; 152(6): 1619-1633.e11, 2023 12.
Artigo
em Inglês
| MEDLINE | ID: mdl-37659505
9.
The 2022 EULAR/ACR points to consider at the early stages of diagnosis and management of suspected haemophagocytic lymphohistiocytosis/macrophage activation syndrome (HLH/MAS).
Ann Rheum Dis
; 82(10): 1271-1285, 2023 10.
Artigo
em Inglês
| MEDLINE | ID: mdl-37487610
10.
T-cell activation profiles distinguish hemophagocytic lymphohistiocytosis and early sepsis.
Blood
; 137(17): 2337-2346, 2021 04 29.
Artigo
em Inglês
| MEDLINE | ID: mdl-33512385
11.
Excessive IL-10 and IL-18 trigger hemophagocytic lymphohistiocytosis-like hyperinflammation and enhanced myelopoiesis.
J Allergy Clin Immunol
; 150(5): 1154-1167, 2022 11.
Artigo
em Inglês
| MEDLINE | ID: mdl-35792218
12.
Comparison of hematopoietic cell transplant conditioning regimens for hemophagocytic lymphohistiocytosis disorders.
J Allergy Clin Immunol
; 149(3): 1097-1104.e2, 2022 03.
Artigo
em Inglês
| MEDLINE | ID: mdl-34375618
13.
Preemptive hematopoietic cell transplantation for asymptomatic patients with X-linked lymphoproliferative syndrome type 1.
Clin Immunol
; 237: 108993, 2022 04.
Artigo
em Inglês
| MEDLINE | ID: mdl-35367395
14.
Risk Factors of Pneumonia in Primary Antibody Deficiency Patients Receiving Immunoglobulin Therapy: Data from the US Immunodeficiency Network (USIDNET).
J Clin Immunol
; 42(7): 1545-1552, 2022 10.
Artigo
em Inglês
| MEDLINE | ID: mdl-35779201
15.
X-Linked Agammaglobulinemia: Infection Frequency and Infection-Related Mortality in the USIDNET Registry.
J Clin Immunol
; 42(4): 827-836, 2022 05.
Artigo
em Inglês
| MEDLINE | ID: mdl-35288819
16.
Reduced-Intensity/Reduced-Toxicity Conditioning Approaches Are Tolerated in XIAP Deficiency but Patients Fare Poorly with Acute GVHD.
J Clin Immunol
; 42(1): 36-45, 2022 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-34586554
17.
Granulocyte Transfusions in Patients with Chronic Granulomatous Disease Undergoing Hematopoietic Cell Transplantation or Gene Therapy.
J Clin Immunol
; 42(5): 1026-1035, 2022 07.
Artigo
em Inglês
| MEDLINE | ID: mdl-35445907
18.
Pediatric hemophagocytic lymphohistiocytosis.
Blood
; 135(16): 1332-1343, 2020 04 16.
Artigo
em Inglês
| MEDLINE | ID: mdl-32107531
19.
Model-informed precision dosing for alemtuzumab in paediatric and young adult patients undergoing allogeneic haematopoietic cell transplantation.
Br J Clin Pharmacol
; 88(1): 248-259, 2022 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-34182590
20.
Test-dose pharmacokinetics guided melphalan dose adjustment in reduced intensity conditioning allogeneic transplant for non-malignant disorders.
Br J Clin Pharmacol
; 88(1): 115-127, 2022 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-34075614