Primary angiitis of the central nervous system: avoiding misdiagnosis and missed diagnosis of a rare disease.
Pract Neurol
; 16(3): 195-200, 2016 Jun.
Article
em En
| MEDLINE
| ID: mdl-26837371
ABSTRACT
Primary angiitis of the central nervous system (PACNS) is an extremely rare condition, defined as a vasculitis limited to the CNS with no identifiable cause. Its presentation is non-specific and includes headache, cognitive dysfunction and focal neurological signs. Laboratory studies, neuroimaging and angiography are neither sufficiently sensitive nor specific for diagnosis; a definitive diagnosis requires brain biopsy. As a result, PACNS is commonly misdiagnosed. Here, we review its clinical, laboratory and radiological features, and focus on avoiding common diagnostic pitfalls.
Palavras-chave
Texto completo:
1
Base de dados:
MEDLINE
Assunto principal:
Vasculite do Sistema Nervoso Central
Tipo de estudo:
Diagnostic_studies
/
Prognostic_studies
Limite:
Humans
Idioma:
En
Ano de publicação:
2016
Tipo de documento:
Article