Gaucher disease: fate of the splenic remnant after partial splenectomy--a case of rapid enlargement.
J Pediatr Surg
; 24(6): 610-2, 1989 Jun.
Article
em En
| MEDLINE
| ID: mdl-2738830
ABSTRACT
In Gaucher disease, partial splenectomy has been suggested for alleviating the complications of splenomegaly as well as for avoiding the immunologic compromise and potential acceleration of bony and hepatic involvement that may follow total splenic resection. However, the fate of the splenic remnant has been reported rarely. A subtotal splenectomy (85%) was performed in a 19-month-old girl with rapidly progressing Gaucher disease and massive splenomegaly (12% of body weight). Within 3 months, the splenic remnant had increased four-fold in size. Previous reports indicated only three Gaucher patients had significant enlargement of the splenic remnant after partial splenectomy. These findings indicate that splenomegaly may recur rapidly in Gaucher disease following partial splenectomy.
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Base de dados:
MEDLINE
Assunto principal:
Esplenectomia
/
Doença de Gaucher
/
Hiperesplenismo
Tipo de estudo:
Etiology_studies
Limite:
Female
/
Humans
/
Infant
Idioma:
En
Ano de publicação:
1989
Tipo de documento:
Article