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An αB-Crystallin Peptide Rescues Compartmentalization and Trafficking Response to Cu Overload of ATP7B-H1069Q, the Most Frequent Cause of Wilson Disease in the Caucasian Population.
Allocca, Simona; Ciano, Michela; Ciardulli, Maria Camilla; D'Ambrosio, Chiara; Scaloni, Andrea; Sarnataro, Daniela; Caporaso, Maria Gabriella; D'Agostino, Massimo; Bonatti, Stefano.
Afiliação
  • Allocca S; Department of Molecular Medicine and Medical Biotechnology, University of Naples Federico II, via S. Pansini 5, 80131 Naples, Italy. simal89@libero.it.
  • Ciano M; Department of Molecular Medicine and Medical Biotechnology, University of Naples Federico II, via S. Pansini 5, 80131 Naples, Italy. michelaciano@libero.it.
  • Ciardulli MC; Department of Molecular Medicine and Medical Biotechnology, University of Naples Federico II, via S. Pansini 5, 80131 Naples, Italy. marikaciardulli93@libero.it.
  • D'Ambrosio C; Proteomics & Mass Spectrometry Laboratory, ISPAAM, National Research Council, Via Argine 1085, 80147 Naples, Italy. chiara.dambrosio@cnr.it.
  • Scaloni A; Proteomics & Mass Spectrometry Laboratory, ISPAAM, National Research Council, Via Argine 1085, 80147 Naples, Italy. andrea.scaloni@ispaam.cnr.it.
  • Sarnataro D; Department of Molecular Medicine and Medical Biotechnology, University of Naples Federico II, via S. Pansini 5, 80131 Naples, Italy. sarnatar@unina.it.
  • Caporaso MG; Ceinge Biotecnologie avanzate scarl, via G. Salvatore 486, 80145 Naples, Italy. sarnatar@unina.it.
  • D'Agostino M; Department of Molecular Medicine and Medical Biotechnology, University of Naples Federico II, via S. Pansini 5, 80131 Naples, Italy. mariagabriella.caporaso@unina.it.
  • Bonatti S; Department of Molecular Medicine and Medical Biotechnology, University of Naples Federico II, via S. Pansini 5, 80131 Naples, Italy. massimo.dagostino@unina.it.
Int J Mol Sci ; 19(7)2018 06 27.
Article em En | MEDLINE | ID: mdl-29954118

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Peptídeos / Cobre / Cadeia B de alfa-Cristalina / ATPases Transportadoras de Cobre / Degeneração Hepatolenticular Limite: Animals / Humans Idioma: En Ano de publicação: 2018 Tipo de documento: Article

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Peptídeos / Cobre / Cadeia B de alfa-Cristalina / ATPases Transportadoras de Cobre / Degeneração Hepatolenticular Limite: Animals / Humans Idioma: En Ano de publicação: 2018 Tipo de documento: Article