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The displacement of frataxin from the mitochondrial cristae correlates with abnormal respiratory supercomplexes formation and bioenergetic defects in cells of Friedreich ataxia patients.
Doni, Davide; Rigoni, Giovanni; Palumbo, Elisa; Baschiera, Elisa; Peruzzo, Roberta; De Rosa, Edith; Caicci, Federico; Passerini, Leonardo; Bettio, Daniela; Russo, Antonella; Szabò, Ildiko; Soriano, Maria Eugenia; Salviati, Leonardo; Costantini, Paola.
Afiliação
  • Doni D; Department of Biology, University of Padova, Padova, Italy.
  • Rigoni G; Department of Biology, University of Padova, Padova, Italy.
  • Palumbo E; Department of Molecular Medicine, University of Padova, Padova, Italy.
  • Baschiera E; Clinical Genetics Unit, Department of Women's and Children's Health, University of Padova, Padova, Italy.
  • Peruzzo R; Istituto di Ricerca Pediatrica (IRP) Città della Speranza, Padova, Italy.
  • De Rosa E; Department of Biology, University of Padova, Padova, Italy.
  • Caicci F; Department of Biology, University of Padova, Padova, Italy.
  • Passerini L; Department of Biology, University of Padova, Padova, Italy.
  • Bettio D; Department of Biology, University of Padova, Padova, Italy.
  • Russo A; Clinical Genetics Unit, Department of Women's and Children's Health, University of Padova, Padova, Italy.
  • Szabò I; Istituto di Ricerca Pediatrica (IRP) Città della Speranza, Padova, Italy.
  • Soriano ME; Department of Molecular Medicine, University of Padova, Padova, Italy.
  • Salviati L; Department of Biology, University of Padova, Padova, Italy.
  • Costantini P; Department of Biology, University of Padova, Padova, Italy.
FASEB J ; 35(3): e21362, 2021 03.
Article em En | MEDLINE | ID: mdl-33629768

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Ataxia de Friedreich / Proteínas de Ligação ao Ferro / Complexo de Proteínas da Cadeia de Transporte de Elétrons / Metabolismo Energético / Membranas Mitocondriais Limite: Humans Idioma: En Ano de publicação: 2021 Tipo de documento: Article

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Ataxia de Friedreich / Proteínas de Ligação ao Ferro / Complexo de Proteínas da Cadeia de Transporte de Elétrons / Metabolismo Energético / Membranas Mitocondriais Limite: Humans Idioma: En Ano de publicação: 2021 Tipo de documento: Article