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النطاق السنوي
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Arq. bras. endocrinol. metab ; Arq. bras. endocrinol. metab;58(6): 646-649, 08/2014. graf
مقالة ي الانجليزية | LILACS | ID: lil-721390

الملخص

We report on a rare case of an adult with severe hypercalcemia secondary to the ectopic secretion of parathyroid-related peptide (PTH-rP) from a penile squamous cell cancer (PC). A patient of 47 years old was admitted with warty lesions and areas of ulceration covered by purulent material in a large area of the groin, scrotum and penis. Laboratory tests revealed severe hypercalcemia and elevation of PTH-rP; the biopsy reported PC. Hypercalcemia was successfully treated with zoledronic acid, however, the tumor displayed aggressive behavior, which resulted in a poor prognosis for the patient.


Relatamos um caso raro em um adulto com hipercalcemia grave secundária à secreção ectópica de peptídeo relacionado ao paratormônio (PTH-rP) de um carcinoma de células escamosas do pênis (CP). Um paciente de 47 anos foi admitido com lesões verrucosas e áreas de ulceração cobertas por material purulento em uma grande área da virilha, escroto e pênis. Os testes laboratoriais revelaram hipercalcemia grave e elevação do PTH-rP; a biópsia mostrou um CP. A hipercalcemia foi tratada de forma bem-sucedida com ácido zoledrônico. Entretanto, o tumor apresentava um comportamento agressivo, resultando em um prognóstico ruim para o paciente.


الموضوعات
Humans , Male , Middle Aged , Carcinoma, Squamous Cell , Hypercalcemia/etiology , Parathyroid Hormone , Penile Neoplasms , Bone Density Conservation Agents/therapeutic use , Diphosphonates/therapeutic use , Hypercalcemia/drug therapy , Imidazoles/therapeutic use , Pelvis , Rare Diseases/etiology , Rare Diseases/metabolism , Tomography, X-Ray Computed
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