الملخص
Cor triatriatum é um anomalia cardíaca congênita rara frequentemente diagnosticada na primeira infância. Este estudo de caso apresenta um adulto com um achado acidental de cor triatriatum sinistrum. Com base na apresentação clínica, o paciente foi tratado de forma conservadora. São apresentados achados de imagens ecocardiográficas de cor triatriatum sinistrum deste paciente juntamente de revisão narrativa da literatura sobre essa doença.(AU)
Cor triatriatum is a rare congenital heart anomaly often diagnosed in early childhood. This case study features an adult with an incidental finding of cor triatriatum sinistrum. Based on the clinical presentation, the patient was treated conservatively. Cor triatriatum sinistrum echocardiographic image findings of this patient are presented along with a narrative review of the literature about this disease. (AU)
الموضوعات
Humans , Male , Middle Aged , Cor Triatriatum/complications , Cor Triatriatum/diagnostic imaging , Incidental Findings , Heart Atria/abnormalities , Magnetic Resonance Spectroscopy/methods , Echocardiography, Doppler/methods , Echocardiography, Transesophageal/methods , Echocardiography, Three-Dimensional/methods , Fatty Liver/complications , Heart Septal Defects, Atrial/complications , Kidney/injuries , Myocardial Infarction/geneticsالموضوعات
Adolescent , Cardiac Surgical Procedures , Cardiopulmonary Bypass , Constriction, Pathologic , Cor Triatriatum/complications , Cor Triatriatum/surgery , Cor Triatriatum/diagnostic imaging , Ductus Arteriosus, Patent/diagnosis , Ductus Arteriosus, Patent/surgery , Ductus Arteriosus, Patent/diagnostic imaging , Echocardiography, Transesophageal , Female , Humans , Hypertension, Pulmonary/complications , Hypertension, Pulmonary/diagnostic imaging , Monitoring, Intraoperative , Oximetry , Pulmonary Veins/pathology , Pulmonary Veins/surgeryالملخص
Thirty nine consecutive cases of congenital left ventricular inflow obstructions (LVIO) diagnosed by two dimensional and Doppler echocardiography are described. The commonest referral diagnosis was severe pulmonary arterial hypertension. Confirmation by cardiac catheterisation and/or surgery was available in twenty one of these cases. The ages ranged from one month to 15 years (mean 3.8 +/- 4.5 years) and 28 were males. Four types of LVIO were defined: i) Congenital mitral stenosis (22 cases). Ventricular septal defect was the commonest association. ii) Cor-triatriatum (7 cases) Out of three patients operated, in one it was found to be a supravalvular mitral ring and not cor-triatriatum as earlier thought on echocardiography. iii) Pulmonary venous obstruction (8 cases). Atrial septal defect and ventricular septal defect were the common associations. iv) Supravalvular mitral ring (2 cases). Double outlet right ventricle and a large ventricular septal defect were associated with one case each. In our experience, two dimensional and Doppler echocardiography is a very useful and reliable investigation for defining the various types of congenital left ventricular inflow obstructions and their hemodynamic significance.