RÉSUMÉ
Amyloidosis is a condition of abnormal deposition of extracellular insoluble fibrillar proteins, termed amyloid, in tissue and organs throughout the body. Systemic amyloidosis, consisting of light amyloid protein (AL protein), the spectrum of multiple myeloma and plasmacytoma, is categorized as a primary amyloidosis; secondary amyloidosis consists of an acute phase reactant serum amyloid A protein (AA protein), which is associated with neoplasm. Amyloid involvement of the tongue is almost always secondary to systemic AL amyloidosis. Macroglossia due to amyloid depositions can lead to serious airway obstruction. We report a case of a 68-year-old woman suffering from dyspnea due to macroglossia. She was diagnosed with amyloidosis associated with multiple myeloma.
Sujet(s)
Femelle , Humains , Obstruction des voies aériennes , Amyloïde , Amyloïdose , Dyspnée , Lumière , Macroglossie , Myélome multiple , Plaque amyloïde , Plasmocytome , Protéines , Protéine amyloïde A sérique , Stress psychologique , LangueRÉSUMÉ
Tracheobronchopathia Osteochondroplastica (TO) is a rare disease of the trachea characterized by the development of submucosal cartilaginous and bony nodules. The nodules are usually located at the anterior and lateral walls and sometims on the posterior membranous wall. Clinically, the manifestations of TO vary from the incidentally detected asymptomatic to life threatening diseases with airway obstruction. Bronchoscopy is a useful diagnostic tool and radiographic studies also play an important role in the diagnosis of TO. The treatment of TO is reserved for the symptomatic lesion with severe airway narrowing and the prevention of recurrent respiratory infections.
Sujet(s)
Obstruction des voies aériennes , Bronchoscopie , Ostéochondrodysplasies , Maladies rares , Infections de l'appareil respiratoire , Trachée , Maladie de la trachéeRÉSUMÉ
Nodular fasciitis is a benign reactive myofibroblastic proliferative lesion of unknown etiology. It is classically presented as a freely mobile, solitary, rapidly growing superficial nodule. It can mimic an early mesenchymal malignancy dut to its rapid growth rate and histologic appearances such as high cellularity and mitotic activity. Nodular fasciitis of the auricular region is uncommon. Here, we describe, along with a literature review, the cases of two patients with nodular fasciitis as a tragal and infrauricular mass.
Sujet(s)
Humains , Oreille externe , Fasciite , Hydrazines , MyofibroblastesRÉSUMÉ
BACKGROUND AND OBJECTIVES: Whether to sacrifice the posterior branch of great auricular nerve (GAN) during parotidectomy is disputatious. This study was to provide a guideline for decision-making. SUBJECTS AND METHOD: Thirty-two patients who underwent parotidectomy due to parotid mass were randomized into two groups. Three patients who underwent further treatment were excluded. Fourteen patients underwent classic parotidectomy by sacrificing GAN whereas 15 patients underwent surgery that preserved the nerve. A two-point discrimination test, sensation of light touch, sharp instrument, blunt instrument and temperature were evaluated preoperatively, and at 7 days, 1, 3, 6, 12 months and 45 months, postoperatively. Patients' preference for the operation time to preserve the nerve was also evaluated. RESULTS: The mean preservation time was 156 seconds. There was no difference in touch sensation, preoperatively, between the two groups. The two-point discrimination test of the infra-auricular area showed significant differences at 1 week postoperatively (p<0.05). The two-point discrimination test of lobule showed significant differences at 1 month (p<0.05), but these differences disappeared at 1 and 3 months. All measured data had no statistically significant differences at 3 and 6 months. At one year, light touch sensation of lobule and temperature sensation of infra-auricular area showed significant differences (p<0.05). Differences in temperature were found at 45 months of follow-up. Of the patients, 95% wanted to preserve the nerve. CONCLUSION: The authors suggest that the posterior branch of GAN was preserved according to patients' preference for the sensation of temperature in the infra-auricular area.