RÉSUMÉ
Amniotic band syndrome (ABS) is a rare congenital disorder which involves fetal entrapment in strands of amniotic tissue, which can manifest as constriction rings, limb and digital amputations or complex congenital anomalies and sometimes results in stillbirth. Etiopathogenesis is varied and ABS can be associated with syndromes. Antenatal diagnosis is made by ultrasonography in most cases. Postnatal examination reveals constrictions, amputations and craniofacial or abdominal wall defects. Treatment is case based and surgical intervention is required to release constriction rings. Authors report here six cases (one stillbirth and five live births) of amniotic band syndrome that were encountered over the last one and half years.
RÉSUMÉ
Congenital constriction bands are anomalous bands that encircle a digit or an extremity. Congenital constriction band syndrome is rare condition and is mostly associated with other musculoskeletal disorders.We report such a rare experience.
RÉSUMÉ
The congenital constriction band syndrome(which is analogous to amniotic band syndrome and Streeter dysplasia), which consist of constriction bands, peripheral lymphedema, acrosyndactyly, club foot, congenital amputation, is thought to be arised as a result of external factors affecting the fetus after early developmental period is completed. Congenital constriction band is rare congenital malformation and has rarely been reported about its occurrence on the adult face. We report a case of constriction band developed in the face and head of a 35-year-old female. Excision and W-plasty was performed for the surgical treatment of this band.