RESUMO
The aim of our study was to examine the spectrum, demographics, and mortality rate among adolescents and adults with congenital heart diseases [CHD] in Oman. Data was collected retrospectively from the Royal Hospital, Muscat, electronic health records for all patients with a diagnosis of CHD aged 13 years and above. Data was analyzed according to the type of CHD and in-hospital mortality was assessed using Kaplan-Meier survival analysis. A total of 600 patients with CHD were identified, among them 145 [24%] were aged 18 years or below. The median age was 24 years. The majority of patients had a simple form of CHD. Atrial and ventricular septal defects together constituted 62.8% of congenital heart diseases. Most patients were clustered in Muscat [32%] and the Batinah regions [31.1%] of Oman. Patients with tetralogy of Fallot and Fontan had shorter survival time than recorded in the published literature. Mostly simple forms of CHD in younger patients was observed. The survival rate was significantly shortened in more complex lesions compared to simple lesions. A national data registry for CHD is needed to address the morbidities and mortality associated with the disease