Primary cutaneous centrofollicular lymphoma with a good response to radiotherapy / Linfoma centrofolicular cutaneo primario com boa resposta a radioterapia
An. bras. dermatol
; An. bras. dermatol;88(6,supl.1): 136-138, Nov-Dec/2013. graf
Article
ي En
| LILACS
| ID: lil-696776
المكتبة المسؤولة:
BR1.1
ABSTRACT
Primary cutaneous lymphomas have different clinical behavior and prognosis than systemic lymphomas of similar histological subtype. About 30% of non-Hodgkin lymphomas involve extranodal tissues, the skin being the second most affected body organ after the gastrointestinal tract (approximately 18%). According to the EORTC (European Organization for Research and Treatment of Cancer) classification, the lymphoma centrofollicular is indolent, since the lesions increase in size slowly over the years and spread to extracutaneous sites is uncommon. Based on this, radiotherapy has been considered the treatment of choice by many studies. We present the case of a patient who had cutaneous centrofollicular scalp lymphoma for 1 year and showed good response to radiotherapy.
RESUMO
Os linfomas cutâneos primários têm comportamento clínico e prognóstico diferente dos linfomas sistêmicos de subtipo histológico semelhante. Cerca de 30% dos linfomas não-Hodgkin acometem tecidos extranodais, sendo a pele o segundo órgão mais envolvido após o trato gastrointestinal (aproximadamente 18%). De acordo com a classificação EORTC (European Organization for Research and Treatment of Cancer), o linfoma centrofolicular cutâneo é indolente, uma vez que as lesões aumentam de tamanho lentamente ao longo dos anos e a disseminação para sitios extracutâneos é incomum. Com base nisso, a radioterapia tem sido apontada como o tratamento de primeira escolha por muitos estudos. Apresentamos um caso de paciente com linfoma cutâneo centrofolicular no couro cabeludo há 1 ano e que apresentou boa resposta à radioterapia.
Key words
النص الكامل:
1
الفهرس:
LILACS
الموضوع الرئيسي:
Scalp
/
Skin Neoplasms
/
Lymphoma, B-Cell
/
Head and Neck Neoplasms
نوع الدراسة:
Prognostic_studies
المحددات:
Humans
/
Male
اللغة:
En
مجلة:
An. bras. dermatol
موضوع المجلة:
DERMATOLOGIA
السنة:
2013
نوع:
Article