A rare case of perineal hamartoma associated with cryptorchidism and imperforate anus: case report / Caso raro de hamartoma perineal associado a criptorquidia e ânus imperfurado: relato de caso
Einstein (Säo Paulo)
; 12(2): 234-236, Apr-Jun/2014. graf
Article
ي En
| LILACS
| ID: lil-713011
المكتبة المسؤولة:
BR1.1
ABSTRACT
A full-term male neonate with anorectal anomaly and external perineal anomalies was referred to our service. Physical examination showed an epithelized perineal mass with cutaneous orifices, which had urine fistulization, hipotrofic perineal musculature, bilateral congenital clubfoot, hipospadic urethra, criptorquidy bilateral with nonpalpable testis and imperforate anus. A colostomy was constructed immediately after birth. The child underwent excision of perineal mass, bilateral orchidopexy, Duplay neourethroplasty and coloanal anastomosis at 3 months of age. The histopathological examination of the perineal mass revealed a hamartoma.
RESUMO
Recém-nascido a termo do sexo masculino encaminhado ao nosso serviço por anomalia anorretal e anomalias perineais externas. O exame físico revelou massa perineal epitelizada, com orifícios cutâneos que apresentavam saída de urina, musculatura perineal hipotrófica, pé torto congênito bilateral, uretra hipospádica, criptorquidia bilateral com testículos não palpáveis e ânus imperfurado. Logo após o nascimento, o paciente foi submetido à colostomia. Aos 3 meses de idade, a criança foi submetida à excisão da massa perineal, orquidopexia bilateral, neouretroplastia a Duplay e anastomose coloanal. A análise anatomopatológica da massa perineal indicou hamartoma.
Key words
النص الكامل:
1
الفهرس:
LILACS
الموضوع الرئيسي:
Anus, Imperforate
/
Perineum
/
Abnormalities, Multiple
/
Cryptorchidism
/
Hamartoma
نوع الدراسة:
Diagnostic_studies
/
Risk_factors_studies
المحددات:
Humans
/
Male
/
Newborn
اللغة:
En
مجلة:
Einstein (Säo Paulo)
موضوع المجلة:
MEDICINA
السنة:
2014
نوع:
Article