Multiple Aortic Operations in Loeys-Dietz Syndrome: Report of 2 Cases
The Korean Journal of Thoracic and Cardiovascular Surgery
; : 536-540, 2014.
Article
ي En
| WPRIM
| ID: wpr-187576
المكتبة المسؤولة:
WPRO
ABSTRACT
Due to its low prevalence and because there is lack of awareness about it, Loeys-Dietz syndrome is often mis-diagnosed as Marfan syndrome, which has similar skeletal abnormalities and aortic pathology. However, the differential diagnosis between these two connective tissue diseases is critical because they correspond to different surgical indications and surgical decision-making. We report two cases of successful thoracoabdominal aortic replacement in patients with previously undiagnosed Loeys-Dietz syndrome.
Key words
النص الكامل:
1
الفهرس:
WPRIM
الموضوع الرئيسي:
Aortic Aneurysm
/
Pathology
/
Prevalence
/
Connective Tissue Diseases
/
Diagnosis, Differential
/
Loeys-Dietz Syndrome
/
Marfan Syndrome
نوع الدراسة:
Diagnostic_studies
/
Prevalence_studies
المحددات:
Humans
اللغة:
En
مجلة:
The Korean Journal of Thoracic and Cardiovascular Surgery
السنة:
2014
نوع:
Article