Linfangiectasia intestinal asociada a hemihipertrofia: Reporte de caso / Intestinal Lymphangiectasia associated with Hemihypertrophy: A case report
Rev. colomb. gastroenterol
;
28(2): 140-148, jun. 2013. ilus, tab
Article
in Spanish
| LILACS
| ID: lil-680527
RESUMEN
La linfangiectasia intestinal primaria es una enfermedad caracterizada por dilatación de los vasos linfáticos del intestino, manifestándose como una enteropatía perdedora de proteínas. Presentamos un paciente con diarrea crónica, prolapso rectal recurrente y hemihipertrofia de miembro superior izquierdo, asociado a linfopenia e hipoalbuminemia. Por endoscopia digestiva superior y biopsia se diagnostica linfangiectasia intestinal primaria y se inicia tratamiento nutricional exitosamente.
ABSTRACT
Primary intestinal lymphangiectasia is a disease characterized by dilated intestinal lymph vessels which manifests as a protein losing enteropathy. We present a patient with chronic diarrhea, recurrent rectal prolapse and left upper limb hemihypertrophy associated with lymphopenia and hypoalbuminemia. Primary intestinal lymphangiectasia was diagnosed with upper endoscopy and biopsy. Nutritional treatment was successfully begun.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Protein-Losing Enteropathies
/
Nutrition Therapy
/
Lymphangiectasis, Intestinal
Type of study:
Risk factors
Limits:
Child, preschool
/
Humans
/
Male
Language:
Spanish
Journal:
Rev. colomb. gastroenterol
Journal subject:
Gastroenterology
Year:
2013
Type:
Article
Affiliation country:
Colombia
Institution/Affiliation country:
Universidad CES/CO
Similar
MEDLINE
...
LILACS
LIS