Rhabdomyosarcoma of Orbit: A Rare Case Report and Review.

ABSTRACT

Rhabdomyosarcoma (RMS) is a highly fulminant, mesenchymal malignant tumor and is considered to be one among life-threatening disease in the present decades. It is considered to be most common malignant neoplasm of the head and neck region with 10% of cases occurring in orbit. Th ough it is common in sixth and seventh decades, it can also occur in early childhood. In this article, we present a rare case of 9-yearold boy who was diagnosed with histopathologically proven RMS of orbit who had undergone a salvage left orbital exenteration following a chemotherapy. Th e main aim of this article is also to provide an overview of RMS of orbit, clinical features, investigations required, staging and various treatment modalities.