Scleromyxedema with Monoclonal Gammopathy / 대한피부과학회지
Korean Journal of Dermatology
;
: 440-443, 2011.
Article
in Korean
| WPRIM
| ID: wpr-34553
ABSTRACT
Scleromyxedema is a rare disorder characterized by generalized papular and sclerodermoid eruption, increased fibroblast proliferation, mucin deposition, and monoclonal gammopathy in the absence of thyroid disease. It is a generalized subtype of lichen myxedematosus. A paraproteinemia, typically an IgG lambda, is observed in more than 80% of patients with scleromyxedema. Here, we report a 38-year-old woman with a 1-year history of a progressively spreading of eruption of small papules on the entire body, including the face, neck, arms, legs, and trunk. Laboratory tests were within normal limits, except lambda light chain monoclonal gammopathy. We administered oral retinoid and topical steroid with slight clinical improvement. To our knowledge, this is the first reported case of scleromyxedema in Korea.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Paraproteinemias
/
Arm
/
Thyroid Diseases
/
Immunoglobulin G
/
Scleromyxedema
/
Fibroblasts
/
Korea
/
Leg
/
Light
/
Mucins
Limits:
Adult
/
Female
/
Humans
Country/Region as subject:
Asia
Language:
Korean
Journal:
Korean Journal of Dermatology
Year:
2011
Type:
Article
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