Early-onset Childhood Sarcoidosis with Incidental Multiple Enchondromatosis
Journal of Korean Medical Science
; : 96-100, 2012.
Article
in En
| WPRIM
| ID: wpr-39059
Responsible library:
WPRO
ABSTRACT
The triad of rash, arthritis, and uveitis seems to be characteristic for early-onset childhood sarcoidosis. We describe an interesting case of early-onset childhood sarcoidosis coexisting enchondromatosis, which clinically masquerade as Langerhans cell histiocytosis. A 33 months old girl presented with skin rash, subcutaneous nodules with polyarthritis, and revealed the involvement of lymph nodes as well as spleen during work-up. She also presented with multiple osteolytic lesions which pathologically proven enchondromatosis. Oral prednisone was prescribed at 2 mg/kg/day for 2 months until when subcutaneous nodules and joint swellings almost disappeared, and then slowly tapered over a period of 5 months. We report an unusual case of early-onset childhood sarcoidosis presented with osteolytic bone lesions which were irrelevant to sarcoidosis.
Key words
Full text:
1
Index:
WPRIM
Main subject:
Arthritis
/
Sarcoidosis
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Prednisone
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Administration, Oral
/
Diagnosis, Differential
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Enchondromatosis
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Whole Body Imaging
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Exanthema
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Positron Emission Tomography Computed Tomography
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Anti-Inflammatory Agents
Type of study:
Diagnostic_studies
Limits:
Child, preschool
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Female
/
Humans
Language:
En
Journal:
Journal of Korean Medical Science
Year:
2012
Type:
Article