An Adrenocorticotropic Hormone-secreting Malignant Pancreatic Neuroendocrine Tumor / 대한내과학회지
Korean Journal of Medicine
; : 238-242, 2011.
Article
in Ko
| WPRIM
| ID: wpr-47586
Responsible library:
WPRO
ABSTRACT
Pancreatic endocrine tumors are low-to-intermediate-grade neoplasms arising from the pancreatic islets that produce various hormones. These tumors account for a minority of pancreatic tumors and are generally considered functional if they are associated with a hormonal syndrome. Adrenocorticotropic hormone-secreting tumors (ACTHomas) are very rare and require special clinical consideration. Patients with ACTH-secreting tumors usually present with Cushing's syndrome, due to ectopic ACTH production. ACTHomas have a poor prognosis because of early metastasis and difficulty controlling corticosteroid production. We report a 62-year-old male with an ACTH-secreting metastatic pancreatic neuroendocrine tumor, who did not respond to somatostatin analogs and died.
Key words
Full text:
1
Index:
WPRIM
Main subject:
Pancreas
/
Prognosis
/
Somatostatin
/
Islets of Langerhans
/
Neuroendocrine Tumors
/
Adrenocorticotropic Hormone
/
Cushing Syndrome
/
Neoplasm Metastasis
Type of study:
Prognostic_studies
Limits:
Humans
/
Male
Language:
Ko
Journal:
Korean Journal of Medicine
Year:
2011
Type:
Article