A case of portal hypertension by presumed as plexiform neurofibroma at the hepatic hilum
Clinical and Molecular Hepatology
; : 276-280, 2016.
Article
in En
| WPRIM
| ID: wpr-56140
Responsible library:
WPRO
ABSTRACT
Neurofibromas can occur anywhere in the body, but they usually involve the head, neck, pelvis, and extremities. Abdominal visceral involvement is rare, and intrahepatic involvement is even less common. We describe a patient who suffered from plexiform neurofibromatosis with liver involvement. A 49-year-old man, who had previously been diagnosed with neurofibromatosis, underwent esophagogastroduodenoscopy and abdominal ultrasonography for screening purposes. Esophagogastroduodenoscopy showed grade 2 esophageal varices and abdominal ultrasonography showed conglomerated nodules with echogenic appearances in the perihepatic space. Magnetic resonance imaging showed presumed plexiform neurofibroma involving the lesser sac and hepatic hilum and encasing the common hepatic artery celiac trunk and superior mesenteric artery left portal triad. We report an unusual case of portal hypertension attributed to the compressive narrowing of the portal vein by presumed as plexiform neurofibroma at the lesser sac and hepatic hilum.
Key words
Full text:
1
Index:
WPRIM
Main subject:
Magnetic Resonance Imaging
/
Esophageal and Gastric Varices
/
Tomography, X-Ray Computed
/
Endoscopy, Digestive System
/
Ultrasonography
/
Neurofibroma, Plexiform
/
Abdomen
/
Hepatic Artery
/
Hypertension, Portal
/
Liver
Type of study:
Diagnostic_studies
Limits:
Humans
/
Male
Language:
En
Journal:
Clinical and Molecular Hepatology
Year:
2016
Type:
Article