Erdheim-Chester Disease Presenting as an Anterior Mediastinal Tumor without Skeletal Involvement
The Korean Journal of Thoracic and Cardiovascular Surgery
; : 223-226, 2018.
Article
in En
| WPRIM
| ID: wpr-715404
Responsible library:
WPRO
ABSTRACT
Erdheim-Chester disease (ECD) is a form of non–Langerhans cell histiocytosis that most commonly involves the skeletal system. We report an unusual case of ECD presenting as an anterior mediastinal tumor without skeletal involvement. A 60-year-old man with no remarkable medical history was referred for evaluation of a mediastinal mass. The patient underwent surgical excision of the tumor via video-assisted thoracoscopic surgery. Histologic examination revealed marked proliferation of atypical histiocytes with sclerosis, and the results of immunohistochemical staining were suggestive of ECD.
Key words
Full text:
1
Index:
WPRIM
Main subject:
Sclerosis
/
Histiocytosis
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Thoracic Surgery, Video-Assisted
/
Erdheim-Chester Disease
/
Histiocytes
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Mediastinum
Limits:
Humans
Language:
En
Journal:
The Korean Journal of Thoracic and Cardiovascular Surgery
Year:
2018
Type:
Article