Primary hepatic malignant peripheral nerve sheath tumor successfully treated with combination therapy: a case report and literature review
Annals of Surgical Treatment and Research
; : 327-331, 2016.
Article
en En
| WPRIM
| ID: wpr-89522
Biblioteca responsable:
WPRO
ABSTRACT
Primary malignant peripheral nerve sheath tumor (MPNST) in a young female patient, not associated with neurofibromatosis type-I is extremely rare in the liver. A 33-year-old female was admitted with a right flank pain for a weak. The CT scan showed 12.5-cm-sized mass located at the right hepatic lobe. At laparotomy, about 20.0-cm-sized mass was on the right hepatic lobe with attachment to right diaphragmatic pleura. Right hepatic lobe and adherent part of diaphragmatic pleura were resected. On histology and immunohistochemistry, it was diagnosed MPNST. Adjuvant radiotherapy for the right diaphragmatic pleura and adjuvant chemotherapy with adriamycin, ifosfamide and cisplatin were sequentially performed. The prognosis of MPNST is generally poor and it is associated with a highly aggressive course of recurrence, metastases, and death. Our case is probably a first report about combination therapy.
Palabras clave
Texto completo:
1
Índice:
WPRIM
Asunto principal:
Nervios Periféricos
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Pleura
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Pronóstico
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Recurrencia
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Inmunohistoquímica
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Doxorrubicina
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Tomografía Computarizada por Rayos X
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Cisplatino
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Quimioterapia Adyuvante
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Neurofibromatosis
Tipo de estudio:
Prognostic_studies
Límite:
Adult
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Female
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Humans
Idioma:
En
Revista:
Annals of Surgical Treatment and Research
Año:
2016
Tipo del documento:
Article