A Case of Primary Intraspinal Peripheral Primitive Neuroectodermal Tumor (pPNET) Mimicking Guillain-Barre Syndrome / 대한소아신경학회지
Journal of the Korean Child Neurology Society
; (4): 326-331, 2010.
Article
de Ko
| WPRIM
| ID: wpr-204568
Bibliothèque responsable:
WPRO
ABSTRACT
Primary intraspinal peripheral primitive neuroectodermal tumors (pPNET) are extremely rare. We report a 10-month-old girl presented with rapidly progressive paraparesis and raised cerebrospinal fluid protein. A magnetic resonance image demonstrated an intramedullary mass from C3 to T3 level and intradural extramedullary nodules in the lumbosacral area. Surgery was performed with partial tumor removal and histologic examination revealed a small round cell tumor and immunohistochemical characteristics of pPNET. She died due to tumor progression at four months after initial diagnosis. This case has been reported to raise awareness among clinicians to include the possibility of intraspinal tumors in the differential diagnosis of progressive neurological deficits mimicking Guillain-Barre syndrome.
Mots clés
Texte intégral:
1
Indice:
WPRIM
Sujet Principal:
Spectroscopie par résonance magnétique
/
Tumeurs neuroectodermiques
/
Tumeurs neuroectodermiques primitives
/
Tumeurs neuroectodermiques primitives périphériques
/
Syndrome de Guillain-Barré
/
Paraparésie
/
Diagnostic différentiel
Type d'étude:
Diagnostic_studies
Limites du sujet:
Humans
/
Infant
langue:
Ko
Texte intégral:
Journal of the Korean Child Neurology Society
Année:
2010
Type:
Article