A Case of Henoch-Schönlein Purpura with Fulminant Complications and Its Long-term Outcome
Childhood Kidney Diseases
; : 128-133, 2019.
Article
de En
| WPRIM
| ID: wpr-785571
Bibliothèque responsable:
WPRO
ABSTRACT
Henoch-Schönlein purpura (HSP) is a systemic vasculitis characterized by purpura, arthritis, abdominal pain, and nephritis. Gastrointestinal involvement can manifest as pain, intussusception, intestinal bleeding, and intestinal perforation. We report a case of fulminant HSP at an age of eight in 1994, with multiple complications of intra-thoracic bleeding, massive intestinal perforation, nephritis, and various skin rashes. The brisk bleeding findings of intestinal on Technetium-99m-labeled red blood cell scan (99mTc RBC scan) were well matched to those of the emergency laparotomy and the resected intestine. The patient's abdominal conditions improved gradually but nodular skin eruptions developed newly apart from improving preexisting lower limb rashes and the urine findings continued abnormal, so skin and kidney biopsy were done for the diagnosis. After cyclosporine therapy, skin eruptions and urine findings returned to normal gradually. On a follow-up after 25 years in 2019, the patient is 33-year-old, healthy without any abnormality on blood chemistries and urine examination.
Mots clés
Texte intégral:
1
Indice:
WPRIM
Sujet Principal:
Arthrite
/
Purpura
/
Peau
/
Biopsie
/
Douleur abdominale
/
Études de suivi
/
Ciclosporine
/
Membre inférieur
/
Diagnostic
/
Urgences
Type d'étude:
Diagnostic_studies
/
Observational_studies
/
Prognostic_studies
Limites du sujet:
Adult
/
Humans
langue:
En
Texte intégral:
Childhood Kidney Diseases
Année:
2019
Type:
Article