Several challenges associated with the anesthetic management of Emery-Dreifuss muscular dystrophy patients: case report
Braz. J. Anesth. (Impr.)
; 73(2): 217-219, March-Apr. 2023. tab
Article
em En
| LILACS
| ID: biblio-1439596
Biblioteca responsável:
BR891.2
ABSTRACT
Abstract Emery-Dreifuss Muscular Dystrophy is a very rare type of muscular dystrophy, associated with contractures, atrophy, and muscle weakness, besides cardiomyopathy with severe arrhythmias. Published studies focusing on this disorder are scarce. We describe the anesthetic management of a male patient with Emery-Dreifuss Muscular Dystrophy, to be submitted to umbilical and inguinal hernioplasty and hydrocele repair under epidural anesthesia. The anesthesia approach enabled us to circumvent the patient's susceptibility to malignant hyperthermia and his potentially difficult airway, in addition to maintaining hemodynamic stability. The day after surgery the patient resumed walking, and two days later he was discharged from the hospital.
Palavras-chave
Texto completo:
1
Índice:
LILACS
Assunto principal:
Distrofia Muscular de Emery-Dreifuss
/
Anestesia Epidural
/
Anestésicos
/
Hipertermia Maligna
Tipo de estudo:
Risk_factors_studies
Limite:
Humans
/
Male
Idioma:
En
Revista:
Braz. J. Anesth. (Impr.)
Ano de publicação:
2023
Tipo de documento:
Article