A difficult airway approach in a merosin-deficient congenital muscular dystrophy patient: a case report
Braz. J. Anesth. (Impr.)
; 73(5): 683-685, 2023. graf
Article
em En
| LILACS
| ID: biblio-1520358
Biblioteca responsável:
BR891.2
ABSTRACT
Abstract Merosin-deficient muscular dystrophy is caused by an autosomal recessive mutation on laminin-α2 gene characterized by severe progressive muscle weakness associated with neuromuscular scoliosis and restrictive lung disease. In this case report, we describe an alternative airway approach performed in a child with anticipated difficult airway and merosin-deficient muscular dystrophy. Significant anesthetic implications may increase the perioperative risk, requiring accurate knowledge to anticipate an adequate management and provide patient-safety strategies.
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Texto completo:
1
Índice:
LILACS
Assunto principal:
Manuseio das Vias Aéreas
Limite:
Child
Idioma:
En
Revista:
Braz. J. Anesth. (Impr.)
Ano de publicação:
2023
Tipo de documento:
Article