Tríada de Carney. Una rara asociación de tumores infrecuentes: caso clínico / Carney triad: report of one case
Rev. méd. Chile
; 145(4): 533-537, abr. 2017. ilus, tab
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| ID: biblio-902507
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ABSTRACT
Carney described a disorder characterized by the presence of several uncommon tumors which were pulmonary chondromas, gastric sarcomas and extra-adrenal paragangliomas. We report a 14 year-old girl in whom multiple gastric tumors were discovered during a study of an iron deficiency anemia and was subjected to a partial gastrectomy. At 25 years of age, she developed several pulmonary chondromas and at 33 years, a mediastinal tumor with features of an extra-adrenal paraganglioma was found. At 35 years of age, a total gastrectomy was performed to remove a gastrointestinal stromal tumor with excision of peritoneal and lymph node metastasis. One year later, the patient died due to liver failure secondary to liver metastases.
Palavras-chave
Texto completo:
1
Índice:
LILACS
Assunto principal:
Neoplasias Gástricas
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Condroma
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Paraganglioma Extrassuprarrenal
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Leiomiossarcoma
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Neoplasias Pulmonares
Limite:
Adolescent
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Female
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Humans
Idioma:
Es
Revista:
Rev. méd. Chile
Assunto da revista:
MEDICINA
Ano de publicação:
2017
Tipo de documento:
Article