Hemophagocytic syndrome: pitfalls in its diagnosis
São Paulo med. j
; 115(5): 1548-52, set.-out. 1997. ilus
Article
em En
| LILACS
| ID: lil-209338
Biblioteca responsável:
BR1.1
ABSTRACT
The hemophagocytic syndrome (HS) is characterized by a clinical picture of fever, hepatospienomegaly, lymphadenopathy and peripheral pancytopenia. The morphologic hallmark of this syndrome is the phagocytosis of hematopoietic elements by morphologically normal macrophages. HS is considered rare and may be a primary disease or associated to viral, infection, neoplasias or autoimmune diseases. Treatment is controversial and its evolution is often fatal. Anatomo-pathological evaluation shows the phenomenon of hemophagocytosis in several organs, especially the hematopoietic tissues. We describe a case of HS, discuss its possible causes, its clinical and pathologic features, its pathophysiology and therapeutic possibilities.
Texto completo:
1
Índice:
LILACS
Assunto principal:
Histiocitose de Células não Langerhans
Tipo de estudo:
Diagnostic_studies
Limite:
Adult
/
Humans
/
Male
Idioma:
En
Revista:
São Paulo med. j
Assunto da revista:
Cirurgia Geral
/
Cincia
/
Ginecologia
/
MEDICINA
/
Medicina Interna
/
Obstetr¡cia
/
Pediatria
/
Sa£de Mental
/
Sa£de P£blica
Ano de publicação:
1997
Tipo de documento:
Article