Clouston syndrome associated with eccrine syringofibroadenoma
An. bras. dermatol
; 89(3): 504-506, May-Jun/2014. graf
Article
em En
| LILACS
| ID: lil-711619
Biblioteca responsável:
BR1.1
ABSTRACT
Eccrine syringofibroadenoma is a rare benign neoplasia derived from acrosyryngium cells of the eccrine sudoriferous glands. It affects the extremities of elderly individuals as solitary tumors, or may also present as multiple lesions. There are controversies about the pathogenesis and differentiation of the tumor. Eccrine syringofibroadenoma has been associated with subjacent conditions, such as for example, hypohidrotic ectodermic dysplasias. The authors describe a case report of a patient with Clouston Syndrome, who presented papules and nodules in extremities, clinically and histologically compatible with eccrine syringofibroadenoma. There are only three cases described in the literature, associated with Clouston Syndrome, and this is the fourth case.
Palavras-chave
Texto completo:
1
Índice:
LILACS
Assunto principal:
Neoplasias das Glândulas Sudoríparas
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Displasia Ectodérmica
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Fibroadenoma
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Glândulas Écrinas
Tipo de estudo:
Risk_factors_studies
Limite:
Adult
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Female
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Humans
Idioma:
En
Revista:
An. bras. dermatol
Assunto da revista:
DERMATOLOGIA
Ano de publicação:
2014
Tipo de documento:
Article