Association between atypical parathyroid adenoma and neurofibromatosis
Arch. endocrinol. metab. (Online)
; 59(5): 460-466, Oct. 2015. tab, graf
Article
em En
| LILACS
| ID: lil-764119
Biblioteca responsável:
BR1.1
ABSTRACT
Primary hyperparathyroidism is a disease characterized by excessive production of parathyroid hormone (PTH), which is due to a parathyroid adenoma in 85% of cases. An atypical parathyroid adenoma, with some histopathological features of parathyroid carcinoma, may be found in some of the cases, although it may not fulfill all the criteria for this diagnosis. Neurofibromatosis type 1 (NF1) is an autosomal dominant systemic disease that may be associated with hyperparathyroidism. We report here the rare combination of a patient with NF1 and clinical manifestations of hyperparathyroidism due to an atypical parathyroid adenoma.
Texto completo:
1
Índice:
LILACS
Assunto principal:
Neoplasias das Paratireoides
/
Adenoma
/
Neurofibromatose 1
Tipo de estudo:
Etiology_studies
/
Risk_factors_studies
Limite:
Female
/
Humans
Idioma:
En
Revista:
Arch. endocrinol. metab. (Online)
Assunto da revista:
ENDOCRINOLOGIA
/
METABOLISMO
Ano de publicação:
2015
Tipo de documento:
Article