Clinical and pathological challenges in the diagnosis of late-onset biliary atresia: four case studies
Braz. j. med. biol. res
; 49(3): e4808, Mar. 2016. tab, graf
Article
em En
| LILACS
| ID: lil-771942
Biblioteca responsável:
BR1.1
ABSTRACT
Biliary atresia (BA) is classically described at the neonatal age. However, rare cases of BA in older infants have also been reported. We report four cases of late-onset BA in infants older than 4 weeks (3 males, 1 female), and describe the diagnostic and management difficulties. One of the cases had a late-onset (29 weeks) presentation with a successful surgical procedure. We highlight the importance of this unusual differential diagnosis in infants with cholestatic syndrome, who may benefit from Kasai surgery, regardless of age.
Palavras-chave
Texto completo:
1
Índice:
LILACS
Assunto principal:
Atresia Biliar
/
Transtornos de Início Tardio
/
Fígado
Tipo de estudo:
Diagnostic_studies
Limite:
Female
/
Humans
/
Infant
/
Male
Idioma:
En
Revista:
Braz. j. med. biol. res
Assunto da revista:
BIOLOGIA
/
MEDICINA
Ano de publicação:
2016
Tipo de documento:
Article