Sporadic lymphangioleiomyomatosis with multiple atypical features: A case report and literature review
Artigo
| IMSEAR
| ID: sea-196139
ABSTRACT
Lymphangioleiomyomatosis (LAM) is a rare, genetically determined, progressive interstitial lung disease, which almost exclusively affects women, especially at the childbearing age. The initial symptoms and radiographic changes in a patient with LAM are always associated with the respiratory system. Here, we present a case of mediastinal and abdominal LAM of a 22-year-old male, where LAM cells are negative for human melanoma black-45 ( HMB-45). The report of this uncharacterized LAM case will make a significant contribution to the realization of LAM associated clinical features, diagnostic approaches, and its afterward treatments.
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Índice:
IMSEAR (Sudeste Asiático)
Ano de publicação:
2018
Tipo de documento:
Artigo
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