Primary Sjö-gren's syndrome presenting with distal, renal tubular acidosis and rhabdomyolysis.
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Primary Sjögren's syndrome (PSS) is rare in India. Clinically manifest renal disease in PSS is uncommon and is usually an autoimmune tubulointerstitial nephritis presenting with distal renal tubular acidosis (dRTA) or a urinary concentrating defect. Hypokalemic paralysis due to dRTA in PSS is rare but well documented in medical literature. Rhabdomyolysis as a consequence of hypokalemia in PSS is exceptional. We report a case of PSS with dRTA and rhabdomyolysis causing prolonged respiratory failure and quadriparesis.
Texto completo:
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Índice:
IMSEAR
Assunto principal:
Rabdomiólise
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Acidose Tubular Renal
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Feminino
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Humanos
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Síndrome de Sjogren
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Diagnóstico Diferencial
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Hipopotassemia
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Pessoa de Meia-Idade
Tipo de estudo:
Diagnostic_studies
Idioma:
En
Ano de publicação:
2006
Tipo de documento:
Article