A Case of Pachydermoperiostosis Combined with Undifferentiated Arthritis
Journal of Rheumatic Diseases
; : 256-259, 2015.
Article
em Ko
| WPRIM
| ID: wpr-10578
Biblioteca responsável:
WPRO
ABSTRACT
Pachydermoperiostosis (PDP) is a primary hypertrophic osteoarthropathy characterized by digital clubbing, pachydermia, and periostosis, which is inherited as an autosomal dominant or recessive trait. We report on a patient suffering from bilateral knee arthritis for 6 years who was newly diagnosed as PDP. PDP was confirmed by bilateral digital clubbing, hyperhidrosis, and cutis verticis gyrata, findings of pachydermatosis on the forehead and scalp, X-ray findings of proliferative periostitis. This case indicates that PDP is one of several possible rare diseases that should be considered in patients with undifferentiated arthritis.
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Texto completo:
1
Índice:
WPRIM
Assunto principal:
Osteoartropatia Hipertrófica Primária
/
Periostite
/
Artrite
/
Couro Cabeludo
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Doenças Raras
/
Testa
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Hiperidrose
/
Joelho
Limite:
Humans
Idioma:
Ko
Revista:
Journal of Rheumatic Diseases
Ano de publicação:
2015
Tipo de documento:
Article