Rosai-Dorfman Disease Combined with Aortic Vasculitis, Arrhythmia, and Valvular Heart Disease
Soonchunhyang Medical Science
; : 31-34, 2014.
Article
em En
| WPRIM
| ID: wpr-107300
Biblioteca responsável:
WPRO
ABSTRACT
Rosai-Dorfman disease (RDD) is a rare and benign self-limited disorder with pathologic feature of the lymph node sinuses expanded by a proliferation of distinctive histiocytes. The most often involving site is bilateral cervical lymphadenopathy, followed by the skin and soft tissue. Treatment options, including steroid, chemotherapy, radiotherapy and debulking surgery depend on the symptoms or the extent and localization of the lesions. We encountered a very rare case of RDD at the skin lesions, particularly combined with aortic vasculitis, arrhythmia, and valvular heart disease.
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Índice:
WPRIM
Assunto principal:
Arritmias Cardíacas
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Radioterapia
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Pele
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Vasculite
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Prednisolona
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Histiocitose Sinusal
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Metotrexato
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Tratamento Farmacológico
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Doenças das Valvas Cardíacas
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Histiócitos
Idioma:
En
Revista:
Soonchunhyang Medical Science
Ano de publicação:
2014
Tipo de documento:
Article