Correction of Frontal Bone Defect in Cleidocranial Dysostosis with Porous Polyethylene(Medpor(R)): A Case Report
Journal of the Korean Society of Plastic and Reconstructive Surgeons
; : 481-484, 2009.
Article
em Ko
| WPRIM
| ID: wpr-119127
Biblioteca responsável:
WPRO
ABSTRACT
PURPOSE: Cleidocranial dysostosis is a rare hereditary disorder affecting bones that develop by intramembranous formation. The typical features include excessive growth of transverse diameter of the skull, hypoplastic clavicles, low height and characteristic facial features. METHODS: A 28-year-old female patient visited by frontal area depression. The diagnosis was performed by computed tomographic study and radiographic imaging. The patient had widely opened anterior fontanelle, partial fused metopic suture, multiple wormian bone and supernumenary impacted teeth. Under the coronal incision, we exposed depressed frontal area and corrected with Medpor block carving. RESULTS: Postoperatively frontoparietal skull was aestheticlly improved and satisfied the patient. CONCLUSION: Authors report a case of cleiodocranial dysostosis who underwent correction of abnormal skull shape by Medpor(R) insertion.
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Assunto principal:
Polietilenos
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Crânio
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Suturas
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Dente Impactado
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Clavícula
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Displasia Cleidocraniana
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Depressão
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Disostoses
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Fontanelas Cranianas
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Osso Frontal
Limite:
Adult
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Female
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Humans
Idioma:
Ko
Revista:
Journal of the Korean Society of Plastic and Reconstructive Surgeons
Ano de publicação:
2009
Tipo de documento:
Article