A Case of Rituximab Treatment for Interstitial Lung Disease in a Patient with Antisynthetase Syndrome / 대한류마티스학회지
The Journal of the Korean Rheumatism Association
; : 448-453, 2010.
Article
em Ko
| WPRIM
| ID: wpr-149517
Biblioteca responsável:
WPRO
ABSTRACT
The clinical manifestations of antisynthetase syndrome are severe interstitial pneumonitis, mild polyarthritis, and myositis. This disease is accompanied by anti-Jo-1 antibodies and anti-Ro/SSA antibodies and occasionally by the concurrence of anti-Jo-1 and anti-Ro/SSA antibodies, which leads to a more severe form of interstitial lung disease. In this case, the patient was transferred to our hospital because of pulmonary fibrosis with myositis and diagnosed with antisynthetase syndrome and the concurrence of anti-Jo-1 with anti-Ro/SSA antibodies. He was refractory to glucocorticoids, and developed leucopenia and thrombocytopenia. He was treated with rituximab infusions, but the interstitial pneumonitis progressed very rapidly and he died.
Palavras-chave
Texto completo:
1
Índice:
WPRIM
Assunto principal:
Artrite
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Fibrose Pulmonar
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Trombocitopenia
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Doenças Pulmonares Intersticiais
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Anticorpos Monoclonais Murinos
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Rituximab
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Glucocorticoides
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Anticorpos
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Miosite
Limite:
Humans
Idioma:
Ko
Revista:
The Journal of the Korean Rheumatism Association
Ano de publicação:
2010
Tipo de documento:
Article