Isolated and Complex Scimitar Vein Anomalies and Their Differentiation from the Meandering Right Pulmonary Vein
Yonsei Medical Journal
; : 973-980, 2007.
Article
em En
| WPRIM
| ID: wpr-154654
Biblioteca responsável:
WPRO
ABSTRACT
PURPOSE: Four pediatric patients with isolated (the adult form) and complex (the infantile form) scimitar vein anomalies were reviewed and compared with patients with meandering right pulmonary veins. MATERIALS AND METHODS: From January 1990 to December 2006, 4 female patients, aged 2 days to 3.5 years, with isolated and complex scimitar vein anomalies were retrospectively studied. The clinical features, chest radiographs, echocardiography, magnetic resonance imaging, magnetic resonance angiography, computer tomography, bronchography, cardiac catheterization with angiography, surgery, and autopsy were reviewed to substantiate the diagnosis of isolated and complex scimitar vein anomalies. RESULTS: Clinical manifestations were lung infections with radiographic scimitar signs in 4 patients (3 right; 1 left), respiratory distress, congestive heart failure, pulmonary hypertension and/or cyanosis in 3 patients, dextrocardia, heterotaxy, and/or right atrial isomerism in 2 patients, as well as dextroversion, right bronchial isomerism, bronchial stenosis, and/or sepsis in 1 patient. Two patients with right atrial isomerism expired. CONCLUSION: The clinical discrimination between scimitar vein anomaly with and without cardiovascular and bronchopulmonary malformations is crucial for the outcomes vary.
Palavras-chave
Texto completo:
1
Índice:
WPRIM
Assunto principal:
Veias Pulmonares
/
Síndrome de Cimitarra
/
Imageamento por Ressonância Magnética
/
Angiografia
/
Ecocardiografia
/
Cateterismo Cardíaco
/
Tomografia Computadorizada por Raios X
/
Estudos Retrospectivos
/
Angiografia por Ressonância Magnética
/
Diagnóstico Diferencial
Tipo de estudo:
Diagnostic_studies
/
Observational_studies
Limite:
Child, preschool
/
Female
/
Humans
/
Infant
/
Newborn
Idioma:
En
Revista:
Yonsei Medical Journal
Ano de publicação:
2007
Tipo de documento:
Article