Death of a Severe Underweight Infant with Pulmonary Interstitial Glycogenosis / 대한법의학회지
Korean Journal of Legal Medicine
; : 178-181, 2012.
Article
em En
| WPRIM
| ID: wpr-224686
Biblioteca responsável:
WPRO
ABSTRACT
Pulmonary interstitial glycogenosis (PIG) is a very rare interstitial lung disease in infants. It is poorly understood, but its pathological features are distinct; they include uniform alveolar septal thickening, caused by a group of oval to spindle-shaped cells containing abundant glycogen, without apparent inflammation or fibrosis. PIG is usually associated with a good prognosis. However, in the present report, we describe the case of a 5-month-old male infant who died due to PIG; he was severely underweight and not administered proper treatment or care. The pathology of PIG was determined following a medico-legal autopsy.
Palavras-chave
Texto completo:
1
Índice:
WPRIM
Assunto principal:
Prognóstico
/
Autopsia
/
Magreza
/
Fibrose
/
Doença de Depósito de Glicogênio
/
Doenças Pulmonares Intersticiais
/
Glicogênio
/
Inflamação
Tipo de estudo:
Prognostic_studies
Limite:
Humans
/
Infant
/
Male
Idioma:
En
Revista:
Korean Journal of Legal Medicine
Ano de publicação:
2012
Tipo de documento:
Article