A Case of Congenital Hepatic Fibrosis Presented with Symptom of Acute Cholangitis / 대한소화기학회지
Korean J. Gastroenterol. (Online)
; : 237-241, 2005.
Article
em Ko
| WPRIM
| ID: wpr-70842
Biblioteca responsável:
WPRO
ABSTRACT
Congenital hepatic fibrosis (CHF) is an autosomal recessive disease, presenting principally in children or young adults with portal hypertension, and infrequently associated with cholangitis. It is associated with renal malformation and Caroli's disease. The diagnosis of CHF is usually confirmed by its typical histological features. Cholangitis is a severe and frequently fatal complication. We report a 22-year-old man with congenital hepatic fibrosis who showed the cholangitis without radiological features of cystic dilatation or stone of intrahepatic ducts.
Palavras-chave
Texto completo:
1
Índice:
WPRIM
Assunto principal:
Colangite
/
Doença Aguda
/
Cirrose Hepática
Tipo de estudo:
Diagnostic_studies
Limite:
Adult
/
Humans
/
Male
Idioma:
Ko
Revista:
Korean J. Gastroenterol. (Online)
Ano de publicação:
2005
Tipo de documento:
Article