Joint Health Status in Hemophilia Patients Using Hemophilia Joint Health Score and Pettersson Score / 임상소아혈액종양
Clinical Pediatric Hematology-Oncology
; : 108-115, 2018.
Article
em Ko
| WPRIM
| ID: wpr-717646
Biblioteca responsável:
WPRO
ABSTRACT
BACKGROUND:
Comprehensive clinical and radiologic follow-up is needed to preserve joint functions and quality of life in hemophilia using clinimetric tools such as Hemophilia joint health score (HJHS) or Pettersson score (PS). We investigated the joint health status evaluated using the tools in Korean hemophilia patients.METHODS:
We reviewed retrospectively medical records to collect clinical parameters, HJHS and PS, who were followed up in Severance Hospital, Seoul, Korea. The correlation between HJHS and PS, and the effect of the prophylaxis for hemophilia on the outcomes measured with the scores were evaluated. The prophylaxis proportion (PP) was calculated as the proportion of prophylaxis duration to each patient's life time.RESULTS:
Total of 28 patients with severe hemophilia were enrolled. Twelve patients (42.8%) were less than 20 years old. Total of 23 patients had experienced prophylaxis during their lives, and median PP was 39.7%. There was significant correlation between HJHS and PS (P 20 years old.CONCLUSION:
HJHS and PS were positively correlated. Each score increased as the patient's age increased. The prophylaxis had protective effect on joint health. The prospective evaluation of HJHS and PS will be needed to prove the effect of proper management on the joint health status.Palavras-chave
Texto completo:
1
Índice:
WPRIM
Assunto principal:
Qualidade de Vida
/
Prontuários Médicos
/
Nível de Saúde
/
Estudos Prospectivos
/
Estudos Retrospectivos
/
Seguimentos
/
Avaliação de Resultados da Assistência ao Paciente
/
Seul
/
Hemofilia A
/
Articulações
Tipo de estudo:
Observational_studies
/
Prognostic_studies
Limite:
Humans
País/Região como assunto:
Asia
Idioma:
Ko
Revista:
Clinical Pediatric Hematology-Oncology
Ano de publicação:
2018
Tipo de documento:
Article