Linfoma intravascular, un desafio diagnóstico: Caso clínico / Intravascular lymphoma: Report of one case
Rev. méd. Chile
; 143(8): 1076-1080, ago. 2015. ilus
Article
в Es
| LILACS
| ID: lil-762674
Ответственная библиотека:
CL1.1
ABSTRACT
Intravascular lymphoma is a rare subtype of extranodal diffuse large B-cell lymphoma characterized by clonal proliferation of lymphocytes inside of small and medium caliber vessels. Its incidence is estimated at one case per million. The clinical picture is very variable, but frequently has skin and central nervous system involvement. It is diagnosed by demonstrating pathological blood vessel infiltration by lymphoma cells. We report a 44 years old male presenting with fever, malaise and erythematous lesions in the abdominal wall. An abdominal wall biopsy showed dilated vascular vessels with atypical cells in their lumen, compatible with large B-cell intravascular lymphoma. He was treated with rituximab, cyclophosphamide, adriamycin, vincristine and prednisone and an autologous hematopoietic stem cell transplantation, achieving a complete remission that has lasted two years.
Key words
Полный текст:
1
База данных:
LILACS
Основная тема:
Lymphoma, Large B-Cell, Diffuse
/
Vascular Neoplasms
Тип исследования:
Diagnostic_studies
Пределы темы:
Adult
/
Humans
/
Male
Язык:
Es
Журнал:
Rev Med Chil
/
Rev. méd. Chile
/
Rev. méd. Chile (En línea)
/
Revista médica de Chile
Тематика журнала:
MEDICINA
Год:
2015
Тип:
Article