Recent advance in primary central nervous system vasculitis with spinal cord involvement / 中华神经医学杂志

ABSTRACT

Primary angiitis of the central nervous system (PACNS) is a rare autoimmune disease of the central nervous system, and spinal cord involvement is a rare subtype. The imaging findings of this subtype lack specificity; it is easily misdiagnosed, missed diagnosed, enjoying high disease recurrence rate, disability and mortality. Therefore, this article reviews the clinical manifestations, diagnoses and treatments of PACNS patients with spinal cord involvement, in order to increase clinicians' understanding of the disease.