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Renal Amyloidosis Secondary to ANCA-Associated Vasculitis: A Case Report / 中国医学科学杂志(英文版)
Article 在 En | WPRIM | ID: wpr-970691
Responsible library: WPRO
ABSTRACT
Renal amyloidosis secondary to anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis is extremely rare. Here, we reported a 77-year-old woman with ANCA-associated vasculitis. Renal biopsy with Masson trichrome staining showed pauci-immune crescentic glomerulonephritis, and electron microscopy showed amyloid deposition in the mesangial area. Immunofluorescence revealed kappa light chain and lambda light chain negative. Bone marrow biopsy revealed no clonal plasma cell. Finally, she was diagnosed as ANCA-associated vasculitis with secondary renal amyloid A amyloidosis.
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全文: 1 索引: WPRIM 主要主题: Antibodies, Antineutrophil Cytoplasmic / Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis / Glomerulonephritis / Amyloidosis / Kidney 限制: Aged / Female / Humans 语言: En 期刊: Chinese Medical Sciences Journal 年: 2022 类型: Article
全文: 1 索引: WPRIM 主要主题: Antibodies, Antineutrophil Cytoplasmic / Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis / Glomerulonephritis / Amyloidosis / Kidney 限制: Aged / Female / Humans 语言: En 期刊: Chinese Medical Sciences Journal 年: 2022 类型: Article