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1.
Elexacaftor/Tezacaftor/Ivacaftor Improved Clinical Outcomes in a Patient with N1303K-CFTR Based on In Vitro Experimental Evidence.
Am J Respir Crit Care Med
; 204(10): 1231-1235, 2021 11 15.
Article
in English
| MEDLINE | ID: mdl-34379998
2.
Compartmentalized accumulation of cAMP near complexes of multidrug resistance protein 4 (MRP4) and cystic fibrosis transmembrane conductance regulator (CFTR) contributes to drug-induced diarrhea.
J Biol Chem
; 290(18): 11246-57, 2015 May 01.
Article
in English
| MEDLINE | ID: mdl-25762723
3.
Personalized medicine in cystic fibrosis: genistein supplementation as a treatment option for patients with a rare S1045Y-CFTR mutation.
Am J Physiol Lung Cell Mol Physiol
; 311(2): L364-74, 2016 Aug 01.
Article
in English
| MEDLINE | ID: mdl-27261451
4.
Altered cGMP dynamics at the plasma membrane contribute to diarrhea in ulcerative colitis.
Am J Pathol
; 185(10): 2790-804, 2015 Oct.
Article
in English
| MEDLINE | ID: mdl-26261085
5.
Asymmetrical macromolecular complex formation of lysophosphatidic acid receptor 2 (LPA2) mediates gradient sensing in fibroblasts.
J Biol Chem
; 289(52): 35757-69, 2014 Dec 26.
Article
in English
| MEDLINE | ID: mdl-25542932
6.
Förster resonance energy transfer - an approach to visualize the spatiotemporal regulation of macromolecular complex formation and compartmentalized cell signaling.
Biochim Biophys Acta
; 1840(10): 3067-72, 2014 Oct.
Article
in English
| MEDLINE | ID: mdl-25086255
7.
Capturing the Direct Binding of CFTR Correctors to CFTR by Using Click Chemistry.
Chembiochem
; 16(14): 2017-22, 2015 Sep 21.
Article
in English
| MEDLINE | ID: mdl-26227551
8.
Drug-induced secretory diarrhea: A role for CFTR.
Pharmacol Res
; 102: 107-112, 2015 Dec.
Article
in English
| MEDLINE | ID: mdl-26429773
9.
Stabilizing rescued surface-localized δf508 CFTR by potentiation of its interaction with Na(+)/H(+) exchanger regulatory factor 1.
Biochemistry
; 53(25): 4169-79, 2014 Jul 01.
Article
in English
| MEDLINE | ID: mdl-24945463
10.
MAST205 competes with cystic fibrosis transmembrane conductance regulator (CFTR)-associated ligand for binding to CFTR to regulate CFTR-mediated fluid transport.
J Biol Chem
; 288(17): 12325-34, 2013 Apr 26.
Article
in English
| MEDLINE | ID: mdl-23504457
11.
Multi-drug resistance protein 4 (MRP4)-mediated regulation of fibroblast cell migration reflects a dichotomous role of intracellular cyclic nucleotides.
J Biol Chem
; 288(6): 3786-94, 2013 Feb 08.
Article
in English
| MEDLINE | ID: mdl-23264633
12.
Human Nephrogenesis can Persist Beyond 40 Postnatal Days in Preterm Infants.
Kidney Int Rep
; 9(2): 436-450, 2024 Feb.
Article
in English
| MEDLINE | ID: mdl-38344733
13.
Compartmentalization of cyclic nucleotide signaling: a question of when, where, and why?
Pflugers Arch
; 465(10): 1397-407, 2013 Oct.
Article
in English
| MEDLINE | ID: mdl-23604972
14.
Characterizing post-branching nephrogenesis in the neonatal rabbit.
Sci Rep
; 13(1): 19234, 2023 11 06.
Article
in English
| MEDLINE | ID: mdl-37932368
15.
The phospholipase A1 activity of lysophospholipase A-I links platelet activation to LPA production during blood coagulation.
J Lipid Res
; 52(5): 958-70, 2011 May.
Article
in English
| MEDLINE | ID: mdl-21393252
16.
Targeting DNAJB9, a novel ER luminal co-chaperone, to rescue ΔF508-CFTR.
Sci Rep
; 9(1): 9808, 2019 07 08.
Article
in English
| MEDLINE | ID: mdl-31285458
17.
Patient-derived pancreas-on-a-chip to model cystic fibrosis-related disorders.
Nat Commun
; 10(1): 3124, 2019 07 16.
Article
in English
| MEDLINE | ID: mdl-31311920
18.
A personalized medicine approach to optimize care for a pediatric cystic fibrosis patient with atypical clinical symptoms.
Pediatr Pulmonol
; 59(1): 229-232, 2024 Jan.
Article
in English
| MEDLINE | ID: mdl-37818777
19.
A young Hispanic with c.1646G>A mutation exhibits severe cystic fibrosis lung disease: is ivacaftor an option for therapy?
Am J Respir Crit Care Med
; 186(7): 694-6, 2012 Oct 01.
Article
in English
| MEDLINE | ID: mdl-23027855
20.
Guanylate cyclase 2C agonism corrects CFTR mutants.
JCI Insight
; 2(19)2017 10 05.
Article
in English
| MEDLINE | ID: mdl-28978796