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1.
Pediatr Surg Int ; 40(1): 193, 2024 Jul 16.
Artículo en Inglés | MEDLINE | ID: mdl-39014287

RESUMEN

PURPOSE: To study the published literature for various models used for simulation and training in the field of pediatric colorectal surgery. METHOD: A PubMed search was conducted for studies of simulation models in anorectal malformation on 24 March 2024 with the search words 'simulation pediatric colorectal surgery' followed by another search on 'simulation AND anorectal malformation' that gave 22 and 14 results, respectively (total 36). After removing 4 duplicate publications, 12 were found relevant to simulation and training in colorectal diseases. One publication relevant to the topic was added from literature, thirteen articles were studied. RESULTS: Of these, 5; 1; 4; and 3 were on inanimate models; animate model; 3D reconstructions; and training, respectively. Simulation models are available for posterior sagittal anorectoplasty. The same inanimate model was used in five articles. The animate model was based on a chicken cadaver. 3D models have been made for personalized preoperative assessment and to understand the imaging in anorectal malformation. One 3D model was made by regeneration of organoid epithelium. Training modules were made to evaluate surgical dissection, standardize surgical techniques, and improve proficiency. CONCLUSION: Simulation models are an important tool for teaching the steps of surgery and discussing the nuances of operative complications among mentors and peers. With advances in this field, the development of high-fidelity models, more training modules, and consensus on surgical techniques will benefit surgical training.


Asunto(s)
Malformaciones Anorrectales , Modelos Anatómicos , Entrenamiento Simulado , Humanos , Malformaciones Anorrectales/cirugía , Entrenamiento Simulado/métodos , Cirugía Colorrectal/educación , Cirugía Colorrectal/métodos
2.
Pediatr Surg Int ; 40(1): 111, 2024 Apr 20.
Artículo en Inglés | MEDLINE | ID: mdl-38641738

RESUMEN

BACKGROUND: Long-term urinary outcomes after anorectal malformation (ARM) repair are affected by surgical approach and sacral anomalies. This study aimed to compare laparoscopic-assisted anorectoplasty (LAARP) and posterior sagittal anorectoplasty (PSARP) in terms of urinary complications. METHODS: Between 2001 and 2022, 45 patients were treated with LAARP or PSARP. The rectourethral fistula and inflow angle between the fistula and rectum was confirmed by preoperative colonography. The incidence of urinary complications and treatment were compared between the two groups. RESULTS: Four patients (14%) had remnant fistula and five patients (17%) had neurogenic bladder dysfunction in LAARP group, while three patients (18%) had urethral injury in PSARP group. All patients with remnant fistula were asymptomatic and followed without treatment. The incidence of remnant fistula improved between earlier decade and later decade. In all cases with urethral injury, suture repair was performed and no postoperative leakage was noted. All five patients with neurogenic bladder dysfunction had spine abnormalities that required clean intermittent catheterization (CIC) and two were free from CIC finally. CONCLUSIONS: It is important to check inflow angle preoperatively to prevent remnant fistula. For PSARP, meticulous dissection is required when separating fistula from urethra because they create common wall. The most contributing factor to neurogenic bladder is sacral anomalies. Preoperative evaluation and postoperative urinary drainage are important.


Asunto(s)
Malformaciones Anorrectales , Laparoscopía , Fístula Rectal , Enfermedades Uretrales , Vejiga Urinaria Neurogénica , Fístula Urinaria , Humanos , Lactante , Recto/cirugía , Recto/anomalías , Malformaciones Anorrectales/complicaciones , Malformaciones Anorrectales/cirugía , Malformaciones Anorrectales/epidemiología , Vejiga Urinaria Neurogénica/etiología , Laparoscopía/efectos adversos , Resultado del Tratamiento , Fístula Rectal/cirugía , Fístula Rectal/complicaciones , Fístula Urinaria/etiología , Fístula Urinaria/cirugía , Enfermedades Uretrales/etiología , Enfermedades Uretrales/cirugía , Complicaciones Posoperatorias/etiología , Uretra/cirugía , Estudios Retrospectivos , Canal Anal/anomalías
3.
Pediatr Surg Int ; 39(1): 277, 2023 Oct 01.
Artículo en Inglés | MEDLINE | ID: mdl-37777986

RESUMEN

PURPOSE: Perioperative and early post-operative outcomes of Primary Posterior sagittal anorectoplasty (P-PSARP) were evaluated. METHOD: Retrospective analysis of cases who underwent P-PSARP from 2004 to 2019 was done. Perioperative care, management, complications, voluntary bowel movement, soiling and constipation, graded by Krickenbeck criteria were studied. RESULTS: One hundred fifty six patients (134 girls) underwent P-PSARP at median age of 5 months (3 months to 14 years) in girls and 5(1-10) days in 21 boys. One male cloaca was operated at 5 months age. Of 20 boys, 5, 8, 4, 3 had rectobulbar urethral fistula, rectoprostatic urethral fistula, bladder neck fistula and male cloaca. Girls had vestibular fistula, rectovaginal fistula, vulval anus, anterior ectopic anus, pouch perineal fistulae and posterior anus with H type fistula in 114, 7, 6, 5, 1 and 1. Complications included wound infection, excoriation, oedema, mucosal prolapse, anal stricture, anal retraction and mortality in 6, 4, 5, 4, 4, 1 and 1, respectively. 35/155(12 neonates) required postoperative dilatations for 5(1-12) months. At follow-up, 96/114(84.2%) had voluntary bowel movements. 46/155 (29.7%) and 9/155 had constipation and soiling. 32:14:0 had grade 1:2:3 constipation, treated with diet (grade 1) and laxatives (grade 2) respectively. 4:3:2 had grade 1:2:3 soiling for initial 3 months, treated with bowel management programme. CONCLUSION: P-PSARP is feasible, subject to proper case selection and good perioperative care, once learning curve is achieved.


Asunto(s)
Malformaciones Anorrectales , Enfermedades de la Próstata , Fístula Rectal , Fístula de la Vejiga Urinaria , Recién Nacido , Femenino , Humanos , Masculino , Lactante , Malformaciones Anorrectales/cirugía , Estudios Retrospectivos , Recto/cirugía , Fístula Rectal/cirugía , Canal Anal/cirugía , Canal Anal/anomalías , Estreñimiento/etiología , Complicaciones Posoperatorias/epidemiología , Complicaciones Posoperatorias/cirugía , Resultado del Tratamiento , Estudios de Seguimiento
4.
Pediatr Surg Int ; 38(12): 1717-1721, 2022 Dec.
Artículo en Inglés | MEDLINE | ID: mdl-36107235

RESUMEN

PURPOSE: The aim of this study was to determine and analyze the stricture rate in patients who underwent a PSARP or PSARVUP and followed a postoperative protocol of anal dilation (Fig. 1). METHODS: A retrospective review of patients with anorectal malformation (ARM) who underwent a primary PSARP or PSARVUP from February 2016 to October 2021 was performed. Data collected included patients' demographics, type of ARM, age at the time of operation, postoperative complications, with emphasis on whether there were any strictures or any difficulties during dilations, and on follow-up. During the surgical repair, emphasis was placed on preserving the blood supply of the bowel and performing a tension-free bowel-to-skin anastomosis. RESULTS: Eighty-four patients met the inclusion criteria. Forty-four patients were females: 21 recto-perineal fistula, 12 cloaca, 9 recto-vestibular fistula, one imperforate anus without fistula, and one patient had a complex anorectal and vaginal malformation with an anal stricture and a rectovaginal fistula. Forty patients were males: 14 recto-perineal fistula, 11 recto-urethral bulbar fistula, 6 recto-urethral prostatic fistula, 6 imperforate anus without fistula, and 2 bladder neck fistula. One patient had an anal stenosis with sacral agenesis, without a presacral mass. Patient ages ranged from 0 to 79 months (mean 7.5 months, median 5 months) at the time of surgery. Follow-up time ranged from 7 to 73 months (mean 38 months, median 35 months). No patient suffered of a postoperative anal stricture. Six patients suffered of a rectal prolapse that required a surgical repair. CONCLUSION: Post-operative anal stricture after PSARP and PSARVUP can be avoided with proper surgical technique and postoperative care. Namely, by preserving adequate blood supply of the bowel and avoiding tension at the anoplasty, and by adhering to a structured protocol of anal dilations.


Asunto(s)
Malformaciones Anorrectales , Ano Imperforado , Laparoscopía , Fístula Rectal , Enfermedades Uretrales , Fístula de la Vejiga Urinaria , Fístula Urinaria , Masculino , Femenino , Humanos , Lactante , Recién Nacido , Preescolar , Niño , Malformaciones Anorrectales/cirugía , Malformaciones Anorrectales/complicaciones , Constricción Patológica/cirugía , Constricción Patológica/complicaciones , Ano Imperforado/cirugía , Dilatación , Laparoscopía/métodos , Fístula Rectal/cirugía , Recto/cirugía , Recto/anomalías , Canal Anal/cirugía , Canal Anal/anomalías , Fístula de la Vejiga Urinaria/complicaciones , Enfermedades Uretrales/cirugía , Fístula Urinaria/cirugía , Estudios Retrospectivos , Complicaciones Posoperatorias/etiología
5.
Pediatr Surg Int ; 36(10): 1255-1260, 2020 Oct.
Artículo en Inglés | MEDLINE | ID: mdl-32638078

RESUMEN

A challenge when repairing imperforate anus is positioning the neo-rectum into the center of the sphincter muscle complex (SMC) with limited muscle injury and scarring. Unfortunately, the path through the components of the SMC are often non-linear. We have used MRI to delineate the complex and guide the needle through the center using standard MRI-guidance (Raschbaum GR et al. J Pediatr Surg 45:220-223, 2010; Thomas TT et al. J Pediatr Surg 35:927-930, 2000). However, asynchronous scanning requires multiple, time-consuming scans to advance the needle in stepwise fashion. Asynchronous scanning also prevents visualizing the needle as it is advanced. We recently integrated software into the MRI operative suite that allows placement of the needle with real-time MRI. We report the feasibility and utility of real-time MRI-assisted laparoscopic assisted anorectoplasty (RT MRI-LAARP). Needle guidance was performed with Siemens Espree 1.5 T MRI with T1 Flash RT Sequence. After needle placement, laparoscopic mobilization, fistula takedown and pull-through was performed using the needle to guide dilation to create a tract to pull-through the neo-rectum. Charts of patients who underwent RT MRI-LAARP were reviewed. Demographics, anatomy, number of needle passes, OR duration and complications are reported. There were five children that underwent RT MRI-LAARP; one was a redo secondary to a retracted rectovestibular fistula. Operative time ranged from 187-505 min. Average hospital stay was 4.0 ± 1.0 days. There were no intraoperative complications although one patient had temporary urinary retention post-op. Muscle sparring laparoscopic anorectoplasty using real-time MRI is feasible and facilitates needle placement through the SMC.


Asunto(s)
Canal Anal/cirugía , Ano Imperforado/cirugía , Laparoscopía/métodos , Imagen por Resonancia Magnética/métodos , Procedimientos de Cirugía Plástica/métodos , Cirugía Asistida por Computador/métodos , Canal Anal/diagnóstico por imagen , Ano Imperforado/diagnóstico , Preescolar , Femenino , Humanos , Lactante , Tiempo de Internación , Masculino , Resultado del Tratamiento
6.
Pediatr Surg Int ; 36(4): 431-445, 2020 Apr.
Artículo en Inglés | MEDLINE | ID: mdl-32086570

RESUMEN

The introduction of posterior sagittal anorectoplasty (PSARP) by deVries and Peña in the early 80s has impacted to the treatment of patients with anorectal malformations (ARM). It gained great recognition worldwide in a very short time, and since then, surgeons dealing with the treatment of this complex malformation could achieve tremendous progress in contemporary management of this anomaly. Despite the growing experience and body of information globally, the treatment of ARMs continues to be a challenge to the pediatric surgeons due to the nature and the variability of the anomaly, and short- and long-term problems continue to exist even after nearly 40 years of the PSARP era. Today, knowing more about it, pediatric surgeons are committed to do more for their ARM patients to have them as physically and socially healthy individuals.


Asunto(s)
Canal Anal/cirugía , Malformaciones Anorrectales/cirugía , Procedimientos Quirúrgicos del Sistema Digestivo/efectos adversos , Procedimientos de Cirugía Plástica/efectos adversos , Complicaciones Posoperatorias , Recto/cirugía , Canal Anal/anomalías , Niño , Humanos , Recto/anomalías
7.
Pol J Radiol ; 83: e348-e352, 2018.
Artículo en Inglés | MEDLINE | ID: mdl-30627258

RESUMEN

Anorectal malformations (ARM) include congenital anomalies of the distal anus and rectum with or without anomalies of the urogenital tract. Posterior sagittal anorectoplasty (PSARP) and minimally invasive laparoscopically assisted anorectal pull-through (LAARP) procedure are now mainly used to surgically treat ARMs. Magnetic resonance imaging (MRI) is the modality of choice for interval follow-up assessment of structural and functional outcome after these surgeries to assess future bowel continence. Well-developed pelvic musculature has been found to be a reflector of better anal continence after ARM surgery. Thus, MRI plays an important role in evaluating the external sphincter complex, puborectalis, and levator ani muscles. Other parameters that need to be noted include the position of the neoanus, rectal diameter, anorectal angle, presence or absence of megarectum, and other ancillary anomalies in the spine. Thus, MRI due to superior soft-tissue resolution is the modality of choice and indispensable for post-operative pelvic evaluation in children.

8.
Pediatr Surg Int ; 33(8): 869-873, 2017 Aug.
Artículo en Inglés | MEDLINE | ID: mdl-28616723

RESUMEN

AIM: For decades, paediatric surgeons have employed the standard posterior sagittal anorectoplasty (PSARP) approach to deal with patients with anorectal malformations (ARM). In recent years, we noted an apparent increase in the incidence of anal stricture after surgical repair of ARM following the introduction of laparoscopic pull-through and techniques aiming to preserve the internal sphincter-the internal sphincter sparing approach (ISSA). We decided to analyse our data to find out if these new trends had added to the problem of post-operative strictures. METHODS: All patients with ARM at our institution from January 2000 to December 2015 were identified. A retrospective case note review was carried out. Data collected included patient demographics, type of ARM, operative details, and post-operative outcomes. RESULTS: 114 patients were identified. Ten patients were excluded. Of the remaining 104 children, 48 (46%) were female. Median age was 8.3 (range 1.2-16.8) years. Types of ARM were as follows: perineal fistula (15 patients), anterior stenotic anus (12), imperforate anus without fistula (10), vestibular fistula (32), rectourethral (bulbar) fistula (11), rectourethral (prostatic) fistula (14), rectovesical fistula (7), and cloaca (3). Twenty-seven patients with a perineal fistula or anterior stenotic anus underwent perineal procedures that were variably described by the different operating surgeons. The majority (15 patients) had an anoplasty, 5 had anal transposition, 5 had limited PSARP, and 2 patients had ISSA. Two patients with a cloacal anomaly underwent open cloacal reconstruction. Of the remaining 75 patients, 45 had a PSARP approach, 6 had a laparoscopic-assisted pull-through, and 18 had ISSA. Four girls with vestibular fistula had anal transposition and two boys with imperforate anus without fistula had anoplasty. 15 (14%) children developed anal stricture. Stricture incidence differed according to operation type. PSARP was the most commonly performed procedure, with only 6% developing a stricture. In contrast, 30% of ISSA patients and 50% of children who had laparoscopic pull-through developed a stricture. Strictures also occurred in 11 and 12% of children having anal transposition and anoplasty, respectively. CONCLUSION: The laparoscopic-assisted pull-through involves tunnelling the sphincter muscle complex. We found that often the tunnels were not wide enough, resulting in narrowing not just at the ano-cutaneous junction but also at the deeper level. 50% developed strictures. We have modified our technique by ensuring that the tunnels are generous enough to allow the rectum to be pulled through without any resistance. ISSA unfortunately resulted in 30% of our patients developing strictures. This approach, started in 2004, was, therefore, abandoned in 2013. The standard Pena's PSARP, with or without a laparotomy, has stood the test of time. Any modification of this approach must be carefully thought through and audited meticulously. Strictures can cause significant morbidity, which may need several revisions, and the resulting redo anoplasties run the risk of sphincter damage, ironically which the newer modifications of ISSA were trying to conserve.


Asunto(s)
Malformaciones Anorrectales/cirugía , Laparoscopía/métodos , Procedimientos de Cirugía Plástica/métodos , Complicaciones Posoperatorias/epidemiología , Adolescente , Malformaciones Anorrectales/epidemiología , Niño , Preescolar , Constricción Patológica/epidemiología , Constricción Patológica/cirugía , Femenino , Humanos , Lactante , Laparoscopía/efectos adversos , Masculino , Complicaciones Posoperatorias/cirugía , Procedimientos de Cirugía Plástica/efectos adversos , Estudios Retrospectivos , Resultado del Tratamiento
9.
Tech Coloproctol ; 20(4): 249-54, 2016 Apr.
Artículo en Inglés | MEDLINE | ID: mdl-26902368

RESUMEN

Rectal atresia and anal stenosis are rare forms of anorectal malformations. The aim of the definitive surgical repair in such cases is to preserve the anal canal, the dentate line, and the sphincter complex. We present a case of rectal atresia and anal stenosis to demonstrate the differences in the operative repair. The techniques described leave the anterior wall of the very distal anal canal untouched in both rectal stenosis and anal atresia; however, the dissection of the rectum differs. The atretic rectum in rectal atresia is mobilized and sutured to the anal canal circumferentially. In anal stenosis, the posterior rectum is mobilized in the form of rectal advancement, and the posterior 180° is anastomosed directly to the skin (as in a standard PSARP) with preservation of the anal canal as the anterior 180° of the final anoplasty. These patients have an excellent prognosis for bowel control and fecal continence, and therefore, complete mobilization and resection of the anal canal must be avoided.


Asunto(s)
Malformaciones Anorrectales/cirugía , Ano Imperforado/cirugía , Procedimientos Quirúrgicos del Sistema Digestivo/métodos , Canal Anal/cirugía , Femenino , Humanos , Lactante , Recto/cirugía
10.
J Indian Assoc Pediatr Surg ; 20(1): 48-50, 2015 Jan.
Artículo en Inglés | MEDLINE | ID: mdl-25552834

RESUMEN

Association of rectal duplication with rectovestibular fistula is rare. A 3-month-old patient underwent primary posterior sagittal anorectoplasty (PSARP) for rectovestibular fistula. During surgery the patient was found to have a rectal duplication (RD). We managed the case by excising the common wall and fenestrating the two lumens together and completed the PSARP.

11.
J Pediatr Surg ; 59(5): 997-1002, 2024 May.
Artículo en Inglés | MEDLINE | ID: mdl-38365475

RESUMEN

BACKGROUND: Anorectal malformations (ARM) are rare and heterogenous which creates a challenge in conducting research and offering recommendations for best practice. The Pediatric Colorectal and Pelvic Learning Consortium (PCPLC) was formed in 2016 to address this challenge and created a shared national data registry to collect information about pediatric colorectal patients. There has been no external validation of the data collected. We sought to evaluate the database by performing a patient matched analysis comparing 30-day outcomes identified in the PCPLC registry with the NSQIP-P database for patients undergoing surgical repair of ARM. METHODS: Patients captured in the PCPLC database from 2016 to 2021 at institutions also participating in NSQIP-P who underwent ARM repair younger than 12 months old were reviewed for 30-day complications. These patients were matched to their NSQIP-P record using their hospital identification number, and records were compared for concordance in identified complications. RESULTS: A total of 591 patient records met inclusion criteria in the PCPLC database. Of these, 180 patients were also reviewed by NSQIP-P. One hundred and fifty-six patient records had no complications recorded. Twenty-four patient records had a complication listed in one or both databases. There was a 91 % concordance rate between databases. When excluding complications not tracked in the PCPLC registry, this agreement improved to 93 %. CONCLUSION: Including all patients evaluated for this subpopulation, a 91 % concordance rate was observed when comparing PCPLC collected complications to NSQIP-P. Future efforts can focus on further validating the data within the PCPLC for other patient populations. LEVEL OF EVIDENCE: V.


Asunto(s)
Malformaciones Anorrectales , Neoplasias Colorrectales , Humanos , Niño , Lactante , Complicaciones Posoperatorias/epidemiología , Complicaciones Posoperatorias/etiología , Malformaciones Anorrectales/cirugía , Malformaciones Anorrectales/complicaciones , Sistema de Registros , Bases de Datos Factuales , Neoplasias Colorrectales/complicaciones , Mejoramiento de la Calidad , Estudios Retrospectivos
12.
J Pediatr Surg ; 57(9): 75-84, 2022 Sep.
Artículo en Inglés | MEDLINE | ID: mdl-35063254

RESUMEN

BACKGROUND: The purpose of this study is to describe all published studies of single-stage procedures for anorectal malformations and to perform a meta-analysis of studies that compared single-stage to staged procedures. METHODS: Searches were conducted in Pubmed, Medline, Embase and CENTRAL. Meta-analysis was performed in RevMan and expressed as forest plots with odds ratios (OR) and 95% confidence intervals (CI). RESULTS: Thirty-eight studies were included in the narrative synthesis. Nine studies were included in the meta-analysis, representing 537 patients. The majority (70%) of patients included in this meta-analysis had either perineal or vestibular fistulas. Surgical site infection (SSI) was defined as any reported infection involving the neoanus (both superficial infection and dehiscence) and occurred in 51 of the 291 patients who underwent single-stage procedures, and 26 of the 244 patients who underwent staged procedure. Meta-analysis showed a 2.2 times higher risk of surgical site infection (SSI) amongst patients who undergo single-stage procedures (OR 2.22, 95% CI 1.26, 3.92). Six of the 293 patients (2%) who underwent single-stage procedures required a rescue ostomy for wound dehiscence. In LMIC the risk of wound dehiscence was three-fold higher in single-stage (36/202) compared to staged procedures (12/126) (OR 3.07, 95% CI 1.42, 6.63). In HIC there was no evidence of an increased risk of wound dehiscence in patients who underwent a single-stage (15/91) compared to a staged procedure (14/118) (OR 1.51, 95% CI 0.65, 3.51). There is no evidence of a difference between single-stage versus staged procedures with regards to functional outcomes including voluntary bowel movements (79/90 versus 111/128), soiling (24/165 versus 20/203) or constipation (27/90 versus 36/128). CONCLUSION: This systematic review provides further evidence that single-stage procedures for selected patients with anorectal malformations are safe. Whilst there is evidence of an increased risk of SSI, this did not translate to a significant difference in long-term functional outcomes. LEVELS OF EVIDENCE: Level II.


Asunto(s)
Malformaciones Anorrectales , Fístula Rectal , Malformaciones Anorrectales/complicaciones , Malformaciones Anorrectales/cirugía , Estreñimiento/etiología , Humanos , Perineo , Fístula Rectal/cirugía , Infección de la Herida Quirúrgica/complicaciones , Infección de la Herida Quirúrgica/etiología
13.
Children (Basel) ; 9(2)2022 Feb 14.
Artículo en Inglés | MEDLINE | ID: mdl-35204973

RESUMEN

PURPOSE: Anorectal malformations (ARM) are one of the most challenging congenital malformations in pediatric surgery. We aimed to assess the research activity on ARM over the last five decades. METHODS: Data on original research publications were retrieved from the Web of Science Core Collection (1970-2020), and analyzed for countries, authors, scientific journals, and top-ten papers. Scientific quantity was assessed by the number of publications. Research quality was estimated from the number of citations, average citation rate per item (ACI), and h-index. RESULTS: A total number of 1595 articles with 19,419 citations (ACI = 12.2; h-index = 54) were identified. The annual number of publications and citations significantly increased over time (p < 0.0001). The USA (n = 386; 24.2%), Japan (n = 153; 9.6%), and China (n = 137; 8.6%) were the most productive countries; and the USA (n = 7850; ACI = 20.3; h-index = 44), Japan (n = 1937; ACI = 12.6; h-index = 21), and the Netherlands (n = 1318; ACI = 17.3; h-index = 22) were the top cited countries. Articles were preferentially published in JPS (n = 391; 24.5%), PSI (n = 181; 11.3%), and EJPS (n = 56; 3.5%). Top-ten cited papers focused on classification (n = 1), surgical technique (n = 3), associated syndromes (n = 2), postoperative outcome (n = 3), and basic research (n = 1). CONCLUSION: This bibliometric study provides valuable insights into the global development of ARM research, and shows that clinical studies and international collaborations dominate in this field.

14.
J Pediatr Surg ; 56(9): 1570-1575, 2021 Sep.
Artículo en Inglés | MEDLINE | ID: mdl-33039105

RESUMEN

BACKGROUND: Anorectal anomalies (ARA) are characterized by different clinical presentations in both sexes with consequently different management protocols. There exist several controversies and different strategies to manage ARA in the female. PURPOSE: To present our experience in managing girls with ARA highlighting the rationale behind the chosen protocol. PATIENTS AND METHODS: The study included 121 girls with ARA who underwent sagittal anorectoplasty during the period 2009 through 2019. Their age ranged from 3 to 57 months (median = 7 months). There were 68 cases with rectoperineal fistula, 51 with rectovestibular fistula, 1 case with rectovaginal fistula and another case without fistula. Preoperative colostomy was performed in only 5 cases (3 rectovestibular; 1 rectovaginal; 1 without fistula). The rest of cases underwent delayed primary sagittal anorectoplasty (beyond the neonatal period). RESULTS: Postoperative wound complications were detected in 14 cases (11.7%). In general, wound complications were more common among the rectoperineal group. Delayed healing problems in the form of mucosal prolapse/ectropion were detected in 10 cases. Thirty-four cases were available for delayed functional assessment. Voluntary bowel control was present in 91% of cases. Constipation was detected in 7 cases (20%) at follow up. Fecal soiling was present in 6 cases (17.6%); 3 of them were associated with constipation. CONCLUSION: Delayed primary repair of rectoperineal and rectovestibular fistula is feasible with low complications. By adopting this protocol of management, we could achieve comparable results while avoiding unnecessary operations during the neonatal period. LEVEL OF EVIDENCE: This is a case series (Level IV Evidence).


Asunto(s)
Malformaciones Anorrectales , Fístula Rectal , Canal Anal/cirugía , Malformaciones Anorrectales/cirugía , Preescolar , Femenino , Estudios de Seguimiento , Humanos , Lactante , Recién Nacido , Masculino , Fístula Rectal/cirugía , Fístula Rectovaginal/cirugía , Recto/cirugía , Estudios Retrospectivos
15.
J Pediatr Surg ; 56(8): 1322-1327, 2021 Aug.
Artículo en Inglés | MEDLINE | ID: mdl-33483103

RESUMEN

BACKGROUND/PURPOSE: In an effort to standardize educational experience, address future physician shortages, and improve quality of care to patients, many surgical specialties are discussing how to maximize exposure to index cases. One solution being explored is telementoring, which requires a well-developed educational curriculum with intraoperative objectives. The American College of Surgery Telementoring Task Force selected anorectal malformation and posterior sagittal anorectoplasty (PSARP) for the repair of imperforate anus as the initial educational focus for this pilot. The purpose of this study was to obtain international consensus on intraoperative learning objectives for a complex surgical procedure. METHODS: A multidisciplinary team of medical educators and pediatric surgery experts created an outline of essential curricular content and intraoperative learning objectives for PSARP in three clinical scenarios. Twelve international subject matter experts were identified meeting strict inclusion criteria. Intraoperative checklists were revised using the modified-Delphi process. RESULTS: After five rounds of modifications to the intraoperative checklists, international consensus was achieved for three different clinical scenarios requiring a PSARP: perineal or vestibular fistula, low prostatic fistula, and bladder neck fistula. CONCLUSIONS: A modified-Delphi approach was successful in generating guidelines for surgical techniques that can be used to standardize intraoperative teaching and expectations for trainees. TYPE OF STUDY: Diagnostic study LEVEL OF EVIDENCE: Level V (expert opinion).


Asunto(s)
Malformaciones Anorrectales , Procedimientos de Cirugía Plástica , Fístula Rectal , Canal Anal/cirugía , Malformaciones Anorrectales/cirugía , Niño , Consenso , Humanos , Fístula Rectal/cirugía , Recto/cirugía , Resultado del Tratamiento
16.
J Pediatr Surg ; 56(8): 1328-1329, 2021 Aug.
Artículo en Inglés | MEDLINE | ID: mdl-33775403

RESUMEN

This is a commentary on the manuscript entitled "Can Complex Surgical Interventions be Standardized? Reaching International Consensus on Posterior Sagittal Anorectoplasty Using a Modified-Delphi Method" by Hanke, R, Ponsky T, Garrison A, et al.


Asunto(s)
Canal Anal , Procedimientos de Cirugía Plástica , Canal Anal/cirugía , Consenso , Humanos , Recto/cirugía , Estudios Retrospectivos , Resultado del Tratamiento
17.
Ann Med Surg (Lond) ; 72: 103057, 2021 Dec.
Artículo en Inglés | MEDLINE | ID: mdl-34820123

RESUMEN

Anorectal malformations are a wide spectrum of disorders, affecting both genders and rare adult presentation as with increased knowledge and advancements, the majority of cases are diagnosed and rectified at birth. This case is a classic example of delayed presentation caused by illiteracy and a lack of adequate health care in rural locations and highlights the uniqueness of this disease, presentation in adult age group and its management and effect on patient psychology and mental health. Because all low anorectal abnormalities can be treated in a single stage, neonatal assessment at birth and early referral to advanced health care centres are critical, with anterior or posterior sagittal anorectoplasty performed by the age of six months. Concerning the anomaly, parent education is an important aspect of patient care.

18.
European J Pediatr Surg Rep ; 8(1): e3-e6, 2020 Jan.
Artículo en Inglés | MEDLINE | ID: mdl-32042545

RESUMEN

Background Despite serious health risks having been described, traditional enemas are still often used in African traditional medicine. We aim to report two cases of complications secondary to traditional enemas, to illustrate how severe the injuries can be, and to describe the use of a Swenson type endoanal pull-through and a posterior sagittal anorectoplasty (PSARP) as surgical options. Case Description A 2-year-old girl presented with a necrotic rectum after a traditional enema administration. At admission, she required a laparotomy, colostomy fashioning, and extensive debridement of her rectum and perineum. She subsequently had a pull-through of the descending colon using a PSARP approach, a covering loop ileostomy, and a Malone Antegrade Continence Enema. The ileostomy was reversed at the age of 3 years of age and she is now clean with rectal washouts. The second case was a one- and a half-year-old boy with full-thickness burns to the perineum and rectum secondary to a hot-water enema. A colostomy was initially brought out and pulled through 7 months post the initial surgery. He is now growing well and is fully continent to stools. Conclusions The potential complications associated with the practice of administering at-home enemas can be quite devastating. A transanal pull-through and a PSARP have been proven to be successful techniques in patients who have suffered rectal burns due to traditional enemas.

19.
Semin Pediatr Surg ; 29(6): 150986, 2020 Dec.
Artículo en Inglés | MEDLINE | ID: mdl-33288132

RESUMEN

Optimal outcomes in the management of children with Anorectal Malformation (ARM) require careful surgical preparation and detailed understanding of the anatomic principles and operative setup. A clear understanding of operative anatomy and surgical principals guides decision making. Adherence to the principles of ARM repair, as well as the application of operative and imaging adjuncts, will yield the safest and most successful approach to ARM. In this review, we detail the surgical preparation, anatomic principles, and surgical management issues unique to ARM.


Asunto(s)
Canal Anal/cirugía , Malformaciones Anorrectales/cirugía , Procedimientos Quirúrgicos del Sistema Digestivo/métodos , Atención Perioperativa/métodos , Procedimientos de Cirugía Plástica/métodos , Recto/cirugía , Canal Anal/anomalías , Canal Anal/anatomía & histología , Canal Anal/diagnóstico por imagen , Malformaciones Anorrectales/diagnóstico por imagen , Niño , Preescolar , Colostomía/métodos , Humanos , Lactante , Recién Nacido , Laparoscopía , Recto/anomalías , Recto/anatomía & histología , Recto/diagnóstico por imagen , Resultado del Tratamiento
20.
J Pediatr Surg ; 55(10): 2159-2165, 2020 Oct.
Artículo en Inglés | MEDLINE | ID: mdl-32682544

RESUMEN

BACKGROUND AND AIM: Patients with a previously repaired anorectal malformation (ARM) can suffer from complications which lead to incontinence. Reoperation can improve the anatomic result, but its impact on functional outcomes is unclear. METHODS: We performed a retrospective cohort study of patients with a previously repaired ARM who underwent redo PSARP at our Center and compared results at initial assessment and 12 months after redo. RESULTS: One hundred fifty-three patients underwent a redo PSARP for anoplasty mislocation (n=93, 61%), stricture (n=55, 36%), remnant of the original fistula (n=28, 18%), or rectal prolapse (n=11, 7%). Post-redo complications included stricture (n=33, 22%) and dehiscence (n=5, 3%). At 1-year post-redo, 75/153 (49%) are on laxatives only, of whom 57 (76%) are continent of stool. Of the remaining 78 (51%) patients, 61 (78%) are clean (≤1 accident per week) on enemas. Interestingly, 16/79 (20%) of patients with expected poor continence potential were continent of stool on laxatives. Overall, 118/153 (77%) are clean after their redo. Quality of life (76.7 vs. 83.8, p=0.05) and Baylor continence (29.2 vs. 17.7, p=<0.0001) scores improved. CONCLUSION: Patients with fecal incontinence after an ARM repair can, with a reoperation, have their anatomy corrected which can restore continence for many, and improve their quality of life. LEVEL OF EVIDENCE: IV. TYPE OF STUDY: Retrospective cohort study.


Asunto(s)
Malformaciones Anorrectales/cirugía , Incontinencia Fecal/cirugía , Fístula/cirugía , Procedimientos de Cirugía Plástica/efectos adversos , Reoperación , Canal Anal/anomalías , Canal Anal/cirugía , Preescolar , Constricción Patológica/etiología , Constricción Patológica/cirugía , Incontinencia Fecal/tratamiento farmacológico , Incontinencia Fecal/etiología , Femenino , Humanos , Laxativos/uso terapéutico , Masculino , Calidad de Vida , Prolapso Rectal/etiología , Prolapso Rectal/cirugía , Recto/anomalías , Recto/cirugía , Reoperación/efectos adversos , Estudios Retrospectivos , Dehiscencia de la Herida Operatoria/etiología , Resultado del Tratamiento
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