Ovarian adrenal rest tissue in congenital adrenal hyperplasia--a patient report.

Claahsen-van der Grinten, H L; Hulsbergen-van de Kaa, C A; Otten, B J

Claahsen-van der Grinten, H L; Hulsbergen-van de Kaa, C A; Otten, B J.

Affiliation

Claahsen-van der Grinten HL; Department of Metabolic and Endocrine Disease and Radboud University, Nijmegen Medical Center, The Netherlands. H.Claahsen@cukz.umcn.nl

J Pediatr Endocrinol Metab ; 19(2): 177-82, 2006 Feb.

Article in En | MEDLINE | ID: mdl-16562593

ABSTRACT

ABSTRACT

We report a young girl who died in an Addisonian crisis due to previously undiagnosed congenital adrenal hyperplasia (CAH), in whom ovarian adrenal rest tissue was detected at postmortem histopathological examination. This is a very rare complication in female patients with CAH with only two previously reported cases.

Subject(s)

Addison Disease/complications; Adrenal Hyperplasia, Congenital/complications; Adrenal Rest Tumor/complications; Ovarian Neoplasms/complications; Addison Disease/pathology; Adrenal Hyperplasia, Congenital/pathology; Adrenal Rest Tumor/pathology; Fatal Outcome; Female; Humans; Infant; Ovarian Neoplasms/pathology

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Database: MEDLINE Main subject: Ovarian Neoplasms / Addison Disease / Adrenal Hyperplasia, Congenital / Adrenal Rest Tumor Limits: Female / Humans / Infant Language: En Year: 2006 Type: Article

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